DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

A81 Atypical virus infections of central nervous system

  • Header · not billable

A81 is not billable. The category heads 10 billable codes in FY2027, grouped under 5 subdivisions.

Index → code

  • Kuru → A81.81
  • Panencephalitis, subacute, sclerosing → A81.1
  • Dawson's (inclusion body) encephalitis → A81.1

Where it sits

  1. Chapter 1 Certain infectious and parasitic diseases (A00-B99)
  2. A80-A89 Viral and prion infections of the central nervous system (A80-A89)
  3. A81 Atypical virus infections of central nervous system
Billable codes
10
Subdivisions
5
CC / MCC codes
10 / 0
HCC V28 codes
10
New FY2027
0
Index entries
40

Codes in A81

  1. A81.0
    Creutzfeldt-Jakob disease
    Header
  2. A81.00
    Creutzfeldt-Jakob disease, unspecified
    BillableCC127
    Inclusion terms 1

    Inclusion terms

    • Jakob-Creutzfeldt disease, unspecified
  3. A81.01
    Variant Creutzfeldt-Jakob disease
    BillableCC127
    Inclusion terms 1

    Inclusion terms

    • vCJD
  4. A81.09
    Other Creutzfeldt-Jakob disease
    BillableCC127
    Inclusion terms 5

    Inclusion terms

    • CJD
    • Familial Creutzfeldt-Jakob disease
    • Iatrogenic Creutzfeldt-Jakob disease
    • Sporadic Creutzfeldt-Jakob disease
    • Subacute spongiform encephalopathy (with dementia)
  5. A81.1
    Subacute sclerosing panencephalitis
    BillableCC127
    Inclusion terms 2

    Inclusion terms

    • Dawson's inclusion body encephalitis
    • Van Bogaert's sclerosing leukoencephalopathy
  6. A81.2
    Progressive multifocal leukoencephalopathy
    BillableCC127
    Inclusion terms 1

    Inclusion terms

    • Multifocal leukoencephalopathy NOS
  7. A81.8
    Other atypical virus infections of central nervous system
    Header
  8. A81.81
    Kuru
    BillableCC127
  9. A81.82
    Gerstmann-Sträussler-Scheinker syndrome
    BillableCC127
    Inclusion terms 1

    Inclusion terms

    • GSS syndrome
  10. A81.83
    Fatal familial insomnia
    BillableCC127
    Inclusion terms 1

    Inclusion terms

    • FFI
  11. A81.89
    Other atypical virus infections of central nervous system
    BillableCC127
  12. A81.9
    Atypical virus infection of central nervous system, unspecified
    BillableCC127
    Inclusion terms 1

    Inclusion terms

    • Prion diseases of the central nervous system NOS

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At A81

Includes

  • diseases of the central nervous system caused by prions

Use additional code

Notes that also apply

Block A80-A89 instructions (Excludes1 3): printed on the block page.

Chapter 1 instructions (Includes 1, Excludes2 5, Use additional code 1): printed on the chapter 1 page.

Index entries

  • Creutzfeldt-Jakob disease or syndrome (with dementia) → A81.00
  • Bodechtel-Guttman disease (subacute sclerosing panencephalitis) → A81.1
  • Dawson's (inclusion body) encephalitis → A81.1
  • Panencephalitis, subacute, sclerosing → A81.1
  • Van Bogaert's leukoencephalopathy (sclerosing) (subacute) → A81.1
  • Kuru → A81.81
  • Gerstmann-Sträussler-Scheinker syndrome (GSS) → A81.82
  • Creutzfeldt-Jakob disease or syndrome (with dementia)variant (vCJD) → A81.01
  • Creutzfeldt-Jakob disease or syndrome (with dementia)familial → A81.09
  • Creutzfeldt-Jakob disease or syndrome (with dementia)iatrogenic → A81.09
  • Creutzfeldt-Jakob disease or syndrome (with dementia)specified NEC → A81.09
  • Creutzfeldt-Jakob disease or syndrome (with dementia)sporadic → A81.09
  • Encephalopathy (acute)spongiform, subacute (viral) → A81.09
  • Disease, diseasedBodechtel-Guttmann (subacute sclerosing panencephalitis) → A81.1
  • Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute)Dawson's (inclusion body) → A81.1
  • Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute)diffuse sclerosing → A81.1
  • Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute)inclusion body → A81.1
  • Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute)subacute sclerosing → A81.1
  • Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute)van Bogaert's → A81.1
  • Leukoencephalitissubacute sclerosing → A81.1
  • Leukoencephalitisvan Bogaert's (sclerosing) → A81.1
  • Leukoencephalopathyvan Bogaert's (sclerosing) → A81.1
  • Leukoencephalopathymultifocal (progressive) → A81.2
  • Leukoencephalopathyprogressive multifocal → A81.2
  • Disease, diseasedkuru → A81.81
  • SyndromeGerstmann-Sträussler-Scheinker (GSS) → A81.82
  • Insomnia (organic)fatal familial (FFI) → A81.83
  • Disease, diseasedprion, central nervous system → A81.9
  • Infection, infected, infective (opportunistic)slow virus → A81.9
  • Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)in (due to)Creutzfeldt-Jakob disease → A81.00
  • Disease, diseasedprion, central nervous systemspecified NEC → A81.89
  • Infection, infected, infective (opportunistic)slow virusspecified NEC → A81.89
  • Infection, infected, infective (opportunistic)atypicalvirus → A81.9
  • Infection, infected, infective (opportunistic)virus, viral NOSslow → A81.9
  • Infection, infected, infective (opportunistic)atypicalvirusspecified type NEC → A81.89
  • Infection, infected, infective (opportunistic)virus, viral NOSslowspecified NEC → A81.89
  • Infection, infected, infective (opportunistic)virus, viral NOScentral nervous systematypical → A81.9
  • Infection, infected, infective (opportunistic)virus, viral NOScentral nervous systemslow virus → A81.9
  • Infection, infected, infective (opportunistic)virus, viral NOScentral nervous systematypicalspecified NEC → A81.89
  • Infection, infected, infective (opportunistic)virus, viral NOScentral nervous systemslow virusspecified NEC → A81.89

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy