DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

E00 Congenital iodine-deficiency syndrome

  • Header · not billable

E00 is not billable. The category heads 4 billable codes in FY2027: the 4 codes directly below it.

Index → code

  • Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic) → E00.9
  • Syndromeiodine-deficiency, congenital → E00.9
  • Myxedema (adult) (idiocy) (infantile) (juvenile)congenital → E00.1

Where it sits

  1. Chapter 4 Endocrine, nutritional and metabolic diseases (E00-E89)
  2. E00-E07 Disorders of thyroid gland (E00-E07)
  3. E00 Congenital iodine-deficiency syndrome
Billable codes
4
Subdivisions
4
CC / MCC codes
0 / 0
HCC V28 codes
0
New FY2027
0
Index entries
11

Codes in E00

  1. E00.0
    Congenital iodine-deficiency syndrome, neurological type
    Billable
    Inclusion terms 1

    Inclusion terms

    • Endemic cretinism, neurological type
  2. E00.1
    Congenital iodine-deficiency syndrome, myxedematous type
    Billable
    Inclusion terms 2

    Inclusion terms

    • Endemic hypothyroid cretinism
    • Endemic cretinism, myxedematous type
  3. E00.2
    Congenital iodine-deficiency syndrome, mixed type
    Billable
    Inclusion terms 1

    Inclusion terms

    • Endemic cretinism, mixed type
  4. E00.9
    Congenital iodine-deficiency syndrome, unspecified
    Billable
    Inclusion terms 2

    Inclusion terms

    • Congenital iodine-deficiency hypothyroidism NOS
    • Endemic cretinism NOS

Sources of each column.

Instructions

At E00

Excludes1

  • subclinical iodine-deficiency hypothyroidism (E02) E02

Use additional code

  • code (F70-F79) to identify associated intellectual disabilities. F70 F79

Notes that also apply

Chapter 4 instructions (Notes 1, Excludes1 1): printed on the chapter 4 page.

Index entries

  • Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic) → E00.9
  • Myxedema (adult) (idiocy) (infantile) (juvenile)congenital → E00.1
  • Syndromeiodine-deficiency, congenital → E00.9
  • Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic)typeneurological → E00.0
  • Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic)typehypothyroid → E00.1
  • Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic)typemyxedematous → E00.1
  • Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic)typemixed → E00.2
  • Myopathyin (due to)cretinism → E00.9 [G73.7]
  • Syndromeiodine-deficiency, congenitaltypeneurological → E00.0
  • Syndromeiodine-deficiency, congenitaltypemyxedematous → E00.1
  • Syndromeiodine-deficiency, congenitaltypemixed → E00.2

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy