DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

G71 Primary disorders of muscles

  • Header · not billable

G71 is not billable. The category heads 28 billable codes in FY2027, grouped under 6 subdivisions.

Index → code

Where it sits

  1. Chapter 6 Diseases of the nervous system (G00-G99)
  2. G70-G73 Diseases of myoneural junction and muscle (G70-G73)
  3. G71 Primary disorders of muscles
Billable codes
28
Subdivisions
6
CC / MCC codes
5 / 0
HCC V28 codes
21
New FY2027
0
Index entries
224

Codes in G71

  1. G71.0
    Muscular dystrophy
    Header
  2. G71.00
    Muscular dystrophy, unspecified
    Billable197
  3. G71.01
    Duchenne or Becker muscular dystrophy
    Billable197
    Inclusion terms 3

    Inclusion terms

    • Autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker muscular dystrophy
    • Benign [Becker] muscular dystrophy
    • Severe [Duchenne] muscular dystrophy
  4. G71.02
    Facioscapulohumeral muscular dystrophy
    Billable197
    Inclusion terms 1

    Inclusion terms

    • Scapulohumeral muscular dystrophy
  5. G71.03
    Limb girdle muscular dystrophies
    Header
  6. G71.031
    Autosomal dominant limb girdle muscular dystrophy
    Billable197
    Inclusion terms 3

    Inclusion terms

    • LGMD D4 calpain-3-related
    • LGMD D5 collagen 6-related
    • Limb girdle muscular dystrophy type 1
  7. G71.032
    Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
    Billable197
    Inclusion terms 3

    Inclusion terms

    • Limb girdle muscular dystrophy type 2A
    • LGMD R1 calpain-3-related
    • Primary calpainopathy
  8. G71.033
    Limb girdle muscular dystrophy due to dysferlin dysfunction
    Billable197
    Inclusion terms 4

    Inclusion terms

    • Dysferlinopathy
    • LGMD R2 dysferlin-related
    • Limb girdle muscular dystrophy type 2B
    • Miyoshi Myopathy type 1
  9. G71.034
    Limb girdle muscular dystrophy due to sarcoglycan dysfunction
    Header
  10. G71.0340
    Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified
    Billable197
    Inclusion terms 1

    Inclusion terms

    • Sarcoglycanopathy, NOS
  11. G71.0341
    Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
    Billable197
    Inclusion terms 3

    Inclusion terms

    • Alpha sarcoglycanopathy
    • Limb-girdle muscular dystrophy due to alpha-sarcoglycan deficiency
    • Limb girdle muscular dystrophy type 2D
  12. G71.0342
    Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
    Billable197
    Inclusion terms 3

    Inclusion terms

    • Beta sarcoglycanopathy
    • Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
    • Limb girdle muscular dystrophy type 2E
  13. G71.0349
    Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
    Billable197
    Inclusion terms 6

    Inclusion terms

    • Delta sarcoglycanopathy
    • Delta-sarcoglycan-related LGMD R6
    • Gamma sarcoglycanopathy
    • Gamma-sarcoglycan-related LGMD R5
    • Limb girdle muscular dystrophy type 2C
    • Limb girdle muscular dystrophy type 2F
  14. G71.035
    Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
    Billable197
    Inclusion terms 4

    Inclusion terms

    • Anoctamin-5-related LGMD R12 R12
    • Anoctaminopathy
    • Autosomal recessive limb girdle muscular dystrophy type 2L
    • Miyoshi myopathy type 3
  15. G71.036
    Limb girdle muscular dystrophy due to fukutin related protein dysfunction
    Billable197
    Inclusion terms 3

    Inclusion terms

    • LGMD R9 FKRP-related
    • Limb girdle muscular dystrophy due to FKRP deficiency
    • Limb girdle muscular dystrophy type 2I
  16. G71.038
    Other limb girdle muscular dystrophy
    Billable197
    Inclusion terms 2

    Inclusion terms

    • LGMD R22 collagen 6-related R22
    • Other autosomal recessive limb girdle muscular dystrophy
  17. G71.039
    Limb girdle muscular dystrophy, unspecified
    Billable197
  18. G71.09
    Other specified muscular dystrophies
    Billable197
    Inclusion terms 7

    Inclusion terms

    • Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]
    • Congenital muscular dystrophy NOS
    • Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber
    • Distal muscular dystrophy
    • Ocular muscular dystrophy
    • Oculopharyngeal muscular dystrophy
    • Scapuloperoneal muscular dystrophy
  19. G71.1
    Myotonic disorders
    Header
  20. G71.11
    Myotonic muscular dystrophy
    Billable197
    Inclusion terms 5

    Inclusion terms

    • Dystrophia myotonica [Steinert]
    • Myotonia atrophica
    • Myotonic dystrophy
    • Proximal myotonic myopathy (PROMM)
    • Steinert disease
  21. G71.12
    Myotonia congenita
    Billable
    Inclusion terms 4

    Inclusion terms

    • Acetazolamide responsive myotonia congenita
    • Dominant myotonia congenita [Thomsen disease]
    • Myotonia levior
    • Recessive myotonia congenita [Becker disease]
  22. G71.13
    Myotonic chondrodystrophy
    Billable
    Inclusion terms 3

    Inclusion terms

    • Chondrodystrophic myotonia
    • Congenital myotonic chondrodystrophy
    • Schwartz-Jampel disease
  23. G71.14
    Drug induced myotonia
    Billable
    Use additional code 1

    Use additional code

    • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5) T36 T50
  24. G71.19
    Other specified myotonic disorders
    Billable
    Inclusion terms 6

    Inclusion terms

    • Myotonia fluctuans
    • Myotonia permanens
    • Neuromyotonia [Isaacs]
    • Paramyotonia congenita (of von Eulenburg)
    • Pseudomyotonia
    • Symptomatic myotonia
  25. G71.2
    Congenital myopathies
    Header
    Excludes2 1

    Excludes2

    • arthrogryposis multiplex congenita (Q74.3) Q74.3
  26. G71.20
    Congenital myopathy, unspecified
    BillableCC197
  27. G71.21
    Nemaline myopathy
    BillableCC197
  28. G71.22
    Centronuclear myopathy
    Header
  29. G71.220
    X-linked myotubular myopathy
    BillableCC197
    Inclusion terms 1

    Inclusion terms

    • Myotubular (centronuclear) myopathy
  30. G71.228
    Other centronuclear myopathy
    BillableCC197
    Inclusion terms 4

    Inclusion terms

    • Autosomal centronuclear myopathy
    • Autosomal dominant centronuclear myopathy
    • Autosomal recessive centronuclear myopathy
    • Centronuclear myopathy, NOS
  31. G71.29
    Other congenital myopathy
    BillableCC197
    Inclusion terms 4

    Inclusion terms

    • Central core disease
    • Minicore disease
    • Multicore disease
    • Multiminicore disease
  32. G71.3
    Mitochondrial myopathy, not elsewhere classified
    Billable
    Excludes1 5

    Excludes1

    • Kearns-Sayre syndrome (H49.81) H49.81
    • Leber's disease (H47.21) H47.21
    • Leigh's encephalopathy (G31.82) G31.82
    • mitochondrial metabolism disorders (E88.4.-) E88.4
    • Reye's syndrome (G93.7) G93.7
  33. G71.8
    Other primary disorders of muscles
    Billable
  34. G71.9
    Primary disorder of muscle, unspecified
    Billable
    Inclusion terms 1

    Inclusion terms

    • Hereditary myopathy NOS

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At G71

Excludes2

  • arthrogryposis multiplex congenita (Q74.3) Q74.3
  • metabolic disorders (E70-E88) E70 E88
  • myositis (M60.-) M60

Notes that also apply

Chapter 6 instructions (Excludes2 8): printed on the chapter 6 page.

Index entries

  • Duchenne-Griesinger disease → G71.01
  • Fascioscapulohumeral myopathy → G71.02
  • Landouzy-Déjérine dystrophy or facioscapulohumeral atrophy → G71.02
  • Pseudohypertrophic muscular dystrophy (Erb's) → G71.02
  • Scapulohumeral myopathy → G71.02
  • Calpainopathy (primary) → G71.032
  • Dysferlinopathy → G71.033
  • Sarcoglycanopathy → G71.0340
  • Anoctaminopathy → G71.035
  • Pseudohypertrophy, muscle → G71.09
  • Batten-Steinert syndrome → G71.11
  • Curschmann (-Batten) (-Steinert) disease or syndrome → G71.11
  • Steinert's disease → G71.11
  • Thomsen disease → G71.12
  • Schwartz (-Jampel) syndrome → G71.13
  • Eulenburg's disease (congenital paramyotonia) → G71.19
  • Neuromyotonia (Isaacs) → G71.19
  • Paramyotonia (congenita) → G71.19
  • Pseudomyotonia → G71.19
  • Von Eulenburg's disease → G71.19
  • Amyotrophia, amyotrophy, amyotrophic → G71.8
  • Dystrophy, dystrophiamuscular → G71.00
  • Becker'sdystrophy → G71.01
  • Disease, diseasedDuchenne-Griesinger → G71.01
  • Dystrophy, dystrophiaautosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker → G71.01
  • Dystrophy, dystrophiaBecker's type → G71.01
  • Dystrophy, dystrophiaDuchenne's type → G71.01
  • Dystrophy, dystrophiaGower's muscular → G71.01
  • Gower'smuscular dystrophy → G71.01
  • Atrophy, atrophic (of)fascioscapulohumeral (Landouzy- Déjérine) → G71.02
  • Atrophy, atrophic (of)Landouzy-Déjérine → G71.02
  • Atrophy, atrophic (of)pseudohypertrophic (muscle) → G71.02
  • Disease, diseasedErb (-Landouzy) → G71.02
  • Dystrophy, dystrophiaErb's → G71.02
  • Dystrophy, dystrophiaLandouzy-Déjérine → G71.02
  • Erb'sdisease → G71.02
  • Erb'spseudohypertrophic muscular dystrophy → G71.02
  • Myopathyfacioscapulohumeral → G71.02
  • Myopathyscapulohumeral → G71.02
  • Calpainopathy (primary)autosomal dominant → G71.031

184 more, longer entries are not listed; the search box finds them by word.

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