DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

I01 Rheumatic fever with heart involvement

  • Header · not billable

I01 is not billable. The category heads 5 billable codes in FY2027: the 5 codes directly below it.

Index → code

  • Bouillaud's disease or syndrome (rheumatic heart disease) → I01.9
  • SyndromeBouillaud's → I01.9
  • Rheumatic (acute) (subacute)coronary arteritis → I01.8

Where it sits

  1. Chapter 9 Diseases of the circulatory system (I00-I99)
  2. I00-I02 Acute rheumatic fever (I00-I02)
  3. I01 Rheumatic fever with heart involvement
Billable codes
5
Subdivisions
5
CC / MCC codes
5 / 0
HCC V28 codes
0
New FY2027
0
Index entries
40

Codes in I01

  1. I01.0
    Acute rheumatic pericarditis
    BillableCC
    Inclusion terms 2, Excludes1 1

    Inclusion terms

    • Any condition in I00 with pericarditis I00
    • Rheumatic pericarditis (acute)

    Excludes1

    • acute pericarditis not specified as rheumatic (I30.-) I30
  2. I01.1
    Acute rheumatic endocarditis
    BillableCC
    Inclusion terms 2

    Inclusion terms

    • Any condition in I00 with endocarditis or valvulitis I00
    • Acute rheumatic valvulitis
  3. I01.2
    Acute rheumatic myocarditis
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Any condition in I00 with myocarditis I00
  4. I01.8
    Other acute rheumatic heart disease
    BillableCC
    Inclusion terms 2

    Inclusion terms

    • Any condition in I00 with other or multiple types of heart involvement I00
    • Acute rheumatic pancarditis
  5. I01.9
    Acute rheumatic heart disease, unspecified
    BillableCC
    Inclusion terms 3

    Inclusion terms

    • Any condition in I00 with unspecified type of heart involvement I00
    • Rheumatic carditis, acute
    • Rheumatic heart disease, active or acute

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At I01

Excludes1

  • chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process. I05 I09

Notes that also apply

Chapter 9 instructions (Excludes2 10): printed on the chapter 9 page.

Index entries

  • Bouillaud's disease or syndrome (rheumatic heart disease) → I01.9
  • Pericarditis (with decompensation) (with effusion)rheumatic (active) (acute) (with effusion) (with pneumonia) → I01.0
  • Rheumatic (acute) (subacute)pericarditis (active) (acute) (with effusion) (with pneumonia) → I01.0
  • Rheumatic (acute) (subacute)coronary arteritis → I01.8
  • Rheumatic (acute) (subacute)pancarditis, acute → I01.8
  • Disease, diseasedBouillaud's (rheumatic heart disease) → I01.9
  • SyndromeBouillaud's → I01.9
  • Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor)rheumatic (active) (acute) (chronic) (subacute)active with heart involvement → I01
  • Pericarditis (with decompensation) (with effusion)acute (hemorrhagic) (nonrheumatic) (Sicca)rheumatic → I01.0
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)acute or subacuterheumatic (aortic) (mitral) (pulmonary) (tricuspid) → I01.1
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea)active or acute → I01.1
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)rheumatic (chronic) (inactive) (with chorea)active or acute (aortic) (mitral) (pulmonary) (tricuspid) → I01.1
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)tricuspid (chronic) (heart) (inactive) (rheumatic) (valve) (with chorea)active or acute → I01.1
  • Stenosis, stenotic (cicatricial)mitral (chronic) (inactive) (valve)active or acute → I01.1
  • Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile)activerheumatic → I01.2
  • Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile)acute or subacute (interstitial)rheumatic → I01.2
  • Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile)rheumatic (chronic) (inactive) (with chorea)active or acute → I01.2
  • Rheumatic (acute) (subacute)myocarditis (chronic) (inactive) (with chorea)active or acute → I01.2
  • Arteritiscoronary (artery)rheumatic → I01.8
  • Pancarditis (acute) (chronic)rheumaticactive or acute → I01.8
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)aortic (heart) (nonrheumatic) (valve)rheumaticactive or acute → I01.1
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)pulmonary (chronic) (heart) (valve)acute or subacuterheumatic → I01.1
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)pulmonary (chronic) (heart) (valve)rheumatic (chronic) (inactive) (with chorea)active or acute → I01.1
  • Insufficiency, insufficientmitral (valve)rheumaticactive or acute → I01.1
  • Degeneration, degenerativemyocardial, myocardium (fatty) (hyaline) (senile)with rheumatic fever (conditions in I00)active, acute or subacute → I01.2
  • Insufficiency, insufficientmyocardial, myocardium (with arteriosclerosis)rheumaticactive, acute, or subacute → I01.2
  • Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile)acute or subacute (interstitial)due tostreptococcus (beta-hemolytic) → I01.2
  • Hypertrophy, hypertrophiccardiac (chronic) (idiopathic)with rheumatic fever (conditions in I00)active → I01.8
  • Hypertrophy, hypertrophiccardiac (chronic) (idiopathic)rheumatic (with chorea)active or acute → I01.8
  • Disease, diseasedheart (organic)rheumatic (chronic) (inactive) (old) (quiescent) (with chorea)active or acute → I01.9
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)aortic (heart) (nonrheumatic) (valve)withmitral diseaseactive or acute → I01.1
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)aortic (heart) (nonrheumatic) (valve)rheumaticwith mitral diseaseactive or acute → I01.1
  • Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea)withaortic (valve) diseaseactive or acute → I01.1
  • Insufficiency, insufficientmyocardial, myocardium (with arteriosclerosis)withrheumatic fever (conditions in I00)active, acute or subacute → I01.2
  • Failure, failedheart (acute) (senile) (sudden)congestivewith rheumatic fever (conditions in I00)active → I01.8
  • Failure, failedheart (acute) (senile) (sudden)congestiverheumatic (chronic) (inactive) (with chorea)active or acute → I01.8
  • Failure, failedventricularleftwith rheumatic fever (conditions in I00)active → I01.8
  • Failure, failedventricularleftrheumatic (chronic) (inactive) (with chorea)active or acute → I01.8
  • Disease, diseasedheart (organic)withrheumatic fever (conditions in I00)active → I01.9
  • Disease, diseasedheart (organic)withrheumatic fever (conditions in I00)activespecified NEC → I01.8

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy