DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

M35 Other systemic involvement of connective tissue

  • Header · not billable

M35 is not billable. The category heads 23 billable codes in FY2027, grouped under 10 subdivisions.

Index → code

Where it sits

  1. Chapter 13 Diseases of the musculoskeletal system and connective tissue (M00-M99)
  2. M30-M36 Systemic connective tissue disorders (M30-M36)
  3. M35 Other systemic involvement of connective tissue
Billable codes
23
Subdivisions
10
CC / MCC codes
7 / 0
HCC V28 codes
3
New FY2027
0
Index entries
63

Codes in M35

  1. M35.0
    Sjögren syndrome
    Header
    Inclusion terms 1, Excludes1 1, Use additional code 1

    Inclusion terms

    • Sicca syndrome

    Excludes1

    • dry mouth, unspecified (R68.2) R68.2

    Use additional code

    • code to identify associated manifestations
  2. M35.00
    Sjögren syndrome, unspecified
    Billable
  3. M35.01
    Sjögren syndrome with keratoconjunctivitis
    Billable
  4. M35.02
    Sjögren syndrome with lung involvement
    Billable280
  5. M35.03
    Sjögren syndrome with myopathy
    BillableCC
  6. M35.04
    Sjögren syndrome with tubulo-interstitial nephropathy
    Billable
    Inclusion terms 1

    Inclusion terms

    • Renal tubular acidosis in sicca syndrome
  7. M35.05
    Sjögren syndrome with inflammatory arthritis
    Billable
  8. M35.06
    Sjögren syndrome with peripheral nervous system involvement
    Billable
  9. M35.07
    Sjögren syndrome with central nervous system involvement
    BillableCC
  10. M35.08
    Sjögren syndrome with gastrointestinal involvement
    Billable
  11. M35.0A
    Sjögren syndrome with glomerular disease
    Billable
  12. M35.0B
    Sjögren syndrome with vasculitis
    Billable
  13. M35.0C
    Sjögren syndrome with dental involvement
    Billable
  14. M35.09
    Sjögren syndrome with other organ involvement
    Billable
  15. M35.1
    Other overlap syndromes
    BillableCC
    Inclusion terms 1, Excludes1 1

    Inclusion terms

    • Mixed connective tissue disease

    Excludes1

    • polyangiitis overlap syndrome (M30.8) M30.8
  16. M35.2
    Behçet's disease
    BillableCC94
  17. M35.3
    Polymyalgia rheumatica
    Billable
    Excludes1 1

    Excludes1

    • polymyalgia rheumatica with giant cell arteritis (M31.5) M31.5
  18. M35.4
    Diffuse (eosinophilic) fasciitis
    Billable
  19. M35.5
    Multifocal fibrosclerosis
    BillableCC
  20. M35.6
    Relapsing panniculitis [Weber-Christian]
    Billable
    Excludes1 2

    Excludes1

    • lupus panniculitis (L93.2) L93.2
    • panniculitis NOS (M79.3-) M79.3
  21. M35.7
    Hypermobility syndrome
    Billable
    Inclusion terms 1, Excludes1 1, Excludes2 1

    Inclusion terms

    • Familial ligamentous laxity

    Excludes1

    • ligamentous laxity, NOS (M24.2-) M24.2

    Excludes2

    • Ehlers-Danlos syndromes (Q79.6-) Q79.6
  22. M35.8
    Other specified systemic involvement of connective tissue
    Header
  23. M35.81
    Multisystem inflammatory syndrome
    BillableCC2
    Inclusion terms 6, Code first 1, Use additional code 4, Code also 10

    Inclusion terms

    • MIS-A
    • MIS-C
    • Multisystem inflammatory syndrome in adults
    • Multisystem inflammatory syndrome in children
    • Pediatric inflammatory multisystem syndrome
    • PIMS

    Code first

    • , if applicable, COVID-19 (U07.1) U07.1

    Use additional code

    • code, if applicable, for:
    • exposure to COVID-19 or SARS-CoV-2 infection (Z20.822) Z20.822
    • personal history of COVID-19 (Z86.16) Z86.16
    • post COVID-19 condition (U09.9) U09.9

    Code also

    • any associated complications such as:
    • acute hepatic failure (K72.0-) K72.0
    • acute kidney failure (N17.-) N17
    • acute myocarditis (I40.-) I40
    • acute respiratory distress syndrome (J80) J80
    • cardiac arrhythmia (I47-I49.-) I47 I49
    • pneumonia due to COVID-19 (J12.82) J12.82
    • severe sepsis (R65.2-) R65.2
    • viral cardiomyopathy (B33.24) B33.24
    • viral pericarditis (B33.23) B33.23
  24. M35.89
    Other specified systemic involvement of connective tissue
    BillableCC
  25. M35.9
    Systemic involvement of connective tissue, unspecified
    Billable
    Inclusion terms 2

    Inclusion terms

    • Autoimmune disease (systemic) NOS
    • Collagen (vascular) disease NOS

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At M35

Excludes1

  • reactive perforating collagenosis (L87.1) L87.1

Notes that also apply

Block M30-M36 instructions (Includes 4, Excludes1 1): printed on the block page.

Chapter 13 instructions (Notes 1, Excludes2 10): printed on the chapter 13 page.

Index entries

  • Behçet's disease or syndrome → M35.2
  • Forestier's disease (rhizomelic pseudopolyarthritis) → M35.3
  • Polymyalgia → M35.3
  • Pseudopolyarthritis, rhizomelic → M35.3
  • Christian-Weber disease → M35.6
  • Weber-Christian disease → M35.6
  • MIS-A → M35.81
  • MIS-C → M35.81
  • Multisystem inflammatory syndrome (in adult) (in children) → M35.81
  • Pediatric inflammatory multisystem syndrome → M35.81
  • PIMS → M35.81
  • Eosinophilia-myalgia syndrome → M35.89
  • Collagenosis, collagen disease (nonvascular) (vascular) → M35.9
  • Dyscollagenosis → M35.9
  • Keratoconjunctivitissicca (Sjögren's) → M35.0-
  • SyndromeSjögren → M35.00
  • Disease, diseasedmixed connective tissue → M35.1
  • Disease, diseasedForestier's (rhizomelic pseudopolyarthritis) → M35.3
  • Polymyalgiarheumatica → M35.3
  • Fasciitisdiffuse (eosinophilic) → M35.4
  • Fibrosclerosismultifocal → M35.5
  • Panniculitis (nodular) (nonsuppurative)relapsing → M35.6
  • Hypermobility, hypermotilitysyndrome → M35.7
  • Syndromehypermobility → M35.7
  • Syndromemultisystem inflammatory (in adults) (in children) → M35.81
  • Syndromepediatric inflammatory multisystem → M35.81
  • Collagenosis, collagen disease (nonvascular) (vascular)specified NEC → M35.89
  • Syndromeeosinophilia-myalgia → M35.89
  • Ataxia, ataxy, ataxicgluten → M35.9 [G32.81]
  • Autoimmunedisease (systemic) → M35.9
  • Disease, diseasedautoimmune (systemic) NOS → M35.9
  • Disease, diseasedcollagen NOS (nonvascular) (vascular) → M35.9
  • Disease, diseasedconnective tissue, systemic (diffuse) → M35.9
  • Disease, diseasedmesenchymal → M35.9
  • Skinhidebound → M35.9
  • Syndromeconnective tissue → M35.9
  • Myopathyin (due to)sicca syndrome → M35.03
  • Myopathyin (due to)Sjögren's syndrome → M35.03
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)tubulo-interstitial (in)Sjögren's syndrome → M35.04
  • Pyelonephritisin (due to)Sjögren's disease → M35.04

23 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy