DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q33 Congenital malformations of lung

  • Header · not billable

Q33 is not billable. The category heads 9 billable codes in FY2027: the 9 codes directly below it.

Index → code

  • Azygoslobe (lung) → Q33.1
  • Honeycomb lungcongenital → Q33.0
  • Deformitylung (congenital) → Q33.9

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q30-Q34 Congenital malformations of the respiratory system (Q30-Q34)
  3. Q33 Congenital malformations of lung
Billable codes
9
Subdivisions
9
CC / MCC codes
2 / 3
HCC V28 codes
0
New FY2027
0
Index entries
32

Codes in Q33

  1. Q33.0
    Congenital cystic lung
    BillableCCExempt
    Inclusion terms 3, Excludes1 2

    Inclusion terms

    • Congenital cystic lung disease
    • Congenital honeycomb lung
    • Congenital polycystic lung disease

    Excludes1

    • cystic fibrosis (E84.0) E84.0
    • cystic lung disease, acquired or unspecified (J98.4) J98.4
  2. Q33.1
    Accessory lobe of lung
    BillableExempt
    Inclusion terms 1

    Inclusion terms

    • Azygos lobe (fissured), lung
  3. Q33.2
    Sequestration of lung
    BillableMCCExempt
  4. Q33.3
    Agenesis of lung
    BillableMCCExempt
    Inclusion terms 1

    Inclusion terms

    • Congenital absence of lung (lobe)
  5. Q33.4
    Congenital bronchiectasis
    BillableCCExempt
  6. Q33.5
    Ectopic tissue in lung
    BillableExempt
  7. Q33.6
    Congenital hypoplasia and dysplasia of lung
    BillableMCCExempt
    Excludes1 1

    Excludes1

    • pulmonary hypoplasia associated with short gestation (P28.0) P28.0
  8. Q33.8
    Other congenital malformations of lung
    BillableExempt
  9. Q33.9
    Congenital malformation of lung, unspecified
    BillableExempt

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Honeycomb lungcongenital → Q33.0
  • Accessory (congenital)lung (lobe) → Q33.1
  • Azygoslobe (lung) → Q33.1
  • Sequestrationlung, congenital → Q33.2
  • Absence (of) (organ or part) (complete or partial)lung (fissure) (lobe) (bilateral) (unilateral) (congenital) → Q33.3
  • Agenesislung (fissure) (lobe) (bilateral) (unilateral) → Q33.3
  • Aplasialung, congenital (bilateral) (unilateral) → Q33.3
  • Bronchiectasis (cylindrical) (diffuse) (fusiform) (localized) (saccular)congenital → Q33.4
  • Ectopic, ectopia (congenital)bone and cartilage in lung → Q33.5
  • Ectopic, ectopia (congenital)tissue in lung → Q33.5
  • Dysplasialung, congenital (not associated with short gestation) → Q33.6
  • Hypoplasia, hypoplasticlung (lobe) (not associated with short gestation) → Q33.6
  • Hypoplasia, hypoplasticpulmonary (not associated with short gestation) → Q33.6
  • Undeveloped, undevelopmentlung → Q33.6
  • Fusion, fused (congenital)lobes, lung → Q33.8
  • Anomaly, anomalous (congenital) (unspecified type)lung (fissure) (lobe) → Q33.9
  • Anomaly, anomalous (congenital) (unspecified type)pulmonary → Q33.9
  • Deformitylung (congenital) → Q33.9
  • Malformation (congenital)lung → Q33.9
  • Cyst (colloid) (mucous) (simple) (retention)bronchogenic (mediastinal) (sequestration)congenital → Q33.0
  • Cyst (colloid) (mucous) (simple) (retention)congenital NEClung → Q33.0
  • Cyst (colloid) (mucous) (simple) (retention)lungcongenital → Q33.0
  • Cysticlung diseasecongenital → Q33.0
  • Polycystic (disease)lungcongenital → Q33.0
  • Developmentimperfect, congenitallungs → Q33.6
  • Inadequate, inadequacydevelopmentlungs → Q33.6
  • Malpositioncongenitallung (lobe) → Q33.8
  • Disease, diseasedlungcongenital → Q33.9
  • Disease, diseasedcysticlungcongenital → Q33.0
  • Disease, diseasedlungcysticcongenital → Q33.0
  • Disease, diseasedlungpolycysticcongenital → Q33.0
  • Disease, diseasedpolycysticlung or pulmonarycongenital → Q33.0

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy