DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q61 Cystic kidney disease

  • Header · not billable

Q61 is not billable. The category heads 11 billable codes in FY2027, grouped under 8 subdivisions.

Index → code

  • Nephronophthisis → Q61.5
  • Meckel-Gruber syndrome → Q61.9
  • Medullary cystic kidney → Q61.5

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q60-Q64 Congenital malformations of the urinary system (Q60-Q64)
  3. Q61 Cystic kidney disease
Billable codes
11
Subdivisions
8
CC / MCC codes
11 / 0
HCC V28 codes
0
New FY2027
0
Index entries
69

Codes in Q61

  1. Q61.0
    Congenital renal cyst
    Header
  2. Q61.00
    Congenital renal cyst, unspecified
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Cyst of kidney NOS (congenital)
  3. Q61.01
    Congenital single renal cyst
    BillableCCExempt
  4. Q61.02
    Congenital multiple renal cysts
    BillableCCExempt
  5. Q61.1
    Polycystic kidney, infantile type
    Header
    Inclusion terms 1

    Inclusion terms

    • Polycystic kidney, autosomal recessive
  6. Q61.11
    Cystic dilatation of collecting ducts
    BillableCCExempt
  7. Q61.19
    Other polycystic kidney, infantile type
    BillableCCExempt
  8. Q61.2
    Polycystic kidney, adult type
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Polycystic kidney, autosomal dominant
  9. Q61.3
    Polycystic kidney, unspecified
    BillableCCExempt
  10. Q61.4
    Renal dysplasia
    BillableCCExempt
    Inclusion terms 4, Excludes1 1

    Inclusion terms

    • Multicystic dysplastic kidney
    • Multicystic kidney (development)
    • Multicystic kidney disease
    • Multicystic renal dysplasia

    Excludes1

  11. Q61.5
    Medullary cystic kidney
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Nephronophthisis
    • Sponge kidney NOS
  12. Q61.8
    Other cystic kidney diseases
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Fibrocystic kidney
    • Fibrocystic renal degeneration or disease
  13. Q61.9
    Cystic kidney disease, unspecified
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Meckel-Gruber syndrome

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At Q61

Excludes1

  • acquired cyst of kidney (N28.1) N28.1
  • Potter's syndrome (Q60.6) Q60.6

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Multicystic kidney (development) → Q61.4
  • Medullary cystic kidney → Q61.5
  • Nephronophthisis → Q61.5
  • Meckel-Gruber syndrome → Q61.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)polycystic → Q61.3
  • Polycystic (disease)degeneration, kidney → Q61.3
  • Polycystic (disease)kidney → Q61.3
  • Dysplasiakidney → Q61.4
  • Dysplasiarenal → Q61.4
  • Cysticmedullary, kidney → Q61.5
  • Spongekidney (medullary) → Q61.5
  • Fibrocystickidney (congenital) → Q61.8
  • Cystickidney (congenital) → Q61.9
  • Cyst (colloid) (mucous) (simple) (retention)congenital NECkidney → Q61.00
  • Cyst (colloid) (mucous) (simple) (retention)kidneycongenital → Q61.00
  • Cyst (colloid) (mucous) (simple) (retention)kidneymore than one (multiple) → Q61.02
  • Cystickidney (congenital)infantile type NEC → Q61.19
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)polycysticchildhood type NEC → Q61.19
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)polycysticinfantile type NEC → Q61.19
  • Polycystic (disease)degeneration, kidneyautosomal recessive (infantile type) NEC → Q61.19
  • Polycystic (disease)kidneyautosomal recessive (childhood type) NEC → Q61.19
  • Polycystic (disease)kidneyinfantile type NEC → Q61.19
  • Cystickidney (congenital)adult type → Q61.2
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)polycysticadult type → Q61.2
  • Polycystic (disease)degeneration, kidneyautosomal dominant (adult type) → Q61.2
  • Polycystic (disease)kidneyautosomal dominant (adult type) → Q61.2
  • Degeneration, degenerativekidneypolycystic → Q61.3
  • Disease, diseasedkidney (functional) (pelvis)polycystic → Q61.3
  • Disease, diseasedpolycystickidney or renal → Q61.3
  • Disease, diseasedrenal (functional) (pelvis)polycystic (congenital) → Q61.3
  • Disease, diseasedkidney (functional) (pelvis)multicystic → Q61.4
  • Dysplasiakidneymulticystic → Q61.4
  • Dysplasiarenalmulticystic → Q61.4
  • Cystickidney (congenital)medullary → Q61.5
  • Disease, diseasedkidney (functional) (pelvis)fibrocystic (congenital) → Q61.8
  • Disease, diseasedrenal (functional) (pelvis)fibrocystic (congenital) → Q61.8
  • Fibrocysticdiseasekidney (congenital) → Q61.8
  • Degeneration, degenerativekidneycystic, congenital → Q61.9
  • Disease, diseasedcystickidney, congenital → Q61.9
  • Disease, diseasedkidney (functional) (pelvis)cystic (congenital) → Q61.9

29 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy