DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

A50 Congenital syphilis

  • Header · not billable

A50 is not billable. The category heads 33 billable codes in FY2027, grouped under 9 subdivisions.

Index → code

Where it sits

  1. Chapter 1 Certain infectious and parasitic diseases (A00-B99)
  2. A50-A64 Infections with a predominantly sexual mode of transmission (A50-A64)
  3. A50 Congenital syphilis
Billable codes
33
Subdivisions
9
CC / MCC codes
27 / 2
HCC V28 codes
1
New FY2027
0
Index entries
201

Codes in A50

  1. A50.0
    Early congenital syphilis, symptomatic
    Header
    Inclusion terms 1

    Inclusion terms

    • Any congenital syphilitic condition specified as early or manifest less than two years after birth.
  2. A50.01
    Early congenital syphilitic oculopathy
    BillableCC
  3. A50.02
    Early congenital syphilitic osteochondropathy
    BillableCC
  4. A50.03
    Early congenital syphilitic pharyngitis
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Early congenital syphilitic laryngitis
  5. A50.04
    Early congenital syphilitic pneumonia
    BillableCC
  6. A50.05
    Early congenital syphilitic rhinitis
    BillableCC
  7. A50.06
    Early cutaneous congenital syphilis
    BillableCC
  8. A50.07
    Early mucocutaneous congenital syphilis
    BillableCC
  9. A50.08
    Early visceral congenital syphilis
    BillableCC
  10. A50.09
    Other early congenital syphilis, symptomatic
    BillableCC
  11. A50.1
    Early congenital syphilis, latent
    Billable
    Inclusion terms 1

    Inclusion terms

    • Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after birth.
  12. A50.2
    Early congenital syphilis, unspecified
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Congenital syphilis NOS less than two years after birth.
  13. A50.3
    Late congenital syphilitic oculopathy
    Header
    Excludes1 1

    Excludes1

    • Hutchinson's triad (A50.53) A50.53
  14. A50.30
    Late congenital syphilitic oculopathy, unspecified
    BillableCC
  15. A50.31
    Late congenital syphilitic interstitial keratitis
    BillableCC
  16. A50.32
    Late congenital syphilitic chorioretinitis
    BillableCC
  17. A50.39
    Other late congenital syphilitic oculopathy
    BillableCC
  18. A50.4
    Late congenital neurosyphilis [juvenile neurosyphilis]
    Header
    Excludes1 1, Use additional code 1

    Excludes1

    • Hutchinson's triad (A50.53) A50.53

    Use additional code

    • code to identify any associated mental disorder
  19. A50.40
    Late congenital neurosyphilis, unspecified
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Juvenile neurosyphilis NOS
  20. A50.41
    Late congenital syphilitic meningitis
    BillableMCC
  21. A50.42
    Late congenital syphilitic encephalitis
    BillableMCC
  22. A50.43
    Late congenital syphilitic polyneuropathy
    BillableCC
  23. A50.44
    Late congenital syphilitic optic nerve atrophy
    BillableCC
  24. A50.45
    Juvenile general paresis
    BillableCC
    Inclusion terms 2

    Inclusion terms

    • Dementia paralytica juvenilis
    • Juvenile taboparetic neurosyphilis
  25. A50.49
    Other late congenital neurosyphilis
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Juvenile tabes dorsalis
  26. A50.5
    Other late congenital syphilis, symptomatic
    Header
    Inclusion terms 1

    Inclusion terms

    • Any congenital syphilitic condition specified as late or manifest two years or more after birth.
  27. A50.51
    Clutton's joints
    BillableCC
  28. A50.52
    Hutchinson's teeth
    BillableCC
  29. A50.53
    Hutchinson's triad
    BillableCC
  30. A50.54
    Late congenital cardiovascular syphilis
    BillableCC
  31. A50.55
    Late congenital syphilitic arthropathy
    BillableCC92
  32. A50.56
    Late congenital syphilitic osteochondropathy
    BillableCC
  33. A50.57
    Syphilitic saddle nose
    BillableCC
  34. A50.59
    Other late congenital syphilis, symptomatic
    BillableCC
  35. A50.6
    Late congenital syphilis, latent
    Billable
    Inclusion terms 1

    Inclusion terms

    • Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after birth.
  36. A50.7
    Late congenital syphilis, unspecified
    Billable
    Inclusion terms 1

    Inclusion terms

    • Congenital syphilis NOS two years or more after birth.
  37. A50.9
    Congenital syphilis, unspecified
    Billable

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

Notes that also apply

Block A50-A64 instructions (Excludes1 2, Excludes2 1): printed on the block page.

Chapter 1 instructions (Includes 1, Excludes2 5, Use additional code 1): printed on the chapter 1 page.

Index entries

  • Parrot's disease (early congenital syphilitic pseudoparalysis) → A50.02
  • Wegner's disease → A50.02
  • Dennie-Marfan syphilitic syndrome → A50.45
  • Clutton's joints → A50.51 [M12.80]
  • Mulberry molars (congenital syphilis) → A50.52
  • Saber, sabre shin or tibia (syphilitic) → A50.56 [M90.86-]
  • Dubois' disease (thymus gland) → A50.59 [E35]
  • Stigmata congenital syphilis → A50.59
  • Disease, diseasedParrot's (syphilitic osteochondritis) → A50.02
  • Disease, diseasedWegner's (syphilitic osteochondritis) → A50.02
  • Epiphysitissyphilitic (congenital) → A50.02
  • Osteochondritissyphilitic (congenital) (early) → A50.02 [M90.80]
  • Osteochondrosissyphilitic (congenital) → A50.02
  • Oxycephaly, oxycephalicsyphilitic, congenital → A50.02
  • Syphilis, syphilitic (acquired)epiphysitis (congenital) (early) → A50.02
  • Syphilis, syphilitic (acquired)osteochondritis (congenital) (early) → A50.02 [M90.80]
  • Catarrh, catarrhal (acute) (febrile) (infectious) (inflammation)due to congenital syphilis → A50.03
  • Pharyngitis (acute) (catarrhal)(gangrenous) (infective) (malignant) (membranous) (phlegmonous) (pseudomembranous) (simple) (subacute) (suppurative) (ulcerative)syphilitic, congenital (early) → A50.03
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)alba → A50.04
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)syphilitic, congenital (early) → A50.04
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)white (congenital) → A50.04
  • Syphilis, syphilitic (acquired)pneumonia, white → A50.04
  • Snuffles (non-syphilitic)syphilitic (infant) → A50.05 [J99]
  • Syphilis, syphilitic (acquired)coryza, congenital → A50.05
  • Pemphigussyphilitic (congenital) → A50.06
  • Rupia (syphilitic)congenital → A50.06
  • Syphilidcongenital → A50.06
  • Syphilidnewborn → A50.06
  • Syphilis, syphilitic (acquired)pemphigus (congenital) → A50.06
  • Chancre (any genital site) (hard) (hunterian) (mixed) (primary) (seronegative) (seropositive) (syphilitic)congenital → A50.07
  • Syphilis, syphilitic (acquired)hepatomegaly, congenital → A50.08
  • Deafmutism (acquired) (congenital) NECsyphilitic, congenital → A50.09
  • Keratitis (nodular) (nonulcerative) (simple) (zonular)syphilitic (congenital) (prenatal) → A50.31
  • Syphilis, syphilitic (acquired)keratitis (congenital) (interstitial) (late) → A50.31
  • Keratoiritissyphilitic → A50.39
  • Neurosyphilis (arrested) (early) (gumma) (late) (latent) (recurrent) (relapse)congenital → A50.40
  • Neurosyphilis (arrested) (early) (gumma) (late) (latent) (recurrent) (relapse)juvenile (asymptomatic) (meningeal) → A50.40
  • Paralysis, paralytic (complete) (incomplete)juvenile general → A50.45
  • Paresisjuvenile (general) → A50.45
  • Tabes, tabeticcongenital → A50.45

161 more, longer entries are not listed; the search box finds them by word.

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