DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

J99 diagnosis code · Billable category · FY2027

J99 Respiratory disorders in diseases classified elsewhere

  • Billable
  • Not CC/MCC
  • HCC 280
  • POA reported

J99 ICD-10 code: a billable diagnosis code in FY2027; the category has no subdivisions.

CC / MCC
Neither
MS-DRG
196-198
HCC V28
280
POA
Reported
Code Editor
Manifestation
Index entries
21

Instructions

At J99

Excludes1

  • respiratory disorders in:
  • amebiasis (A06.5) A06.5
  • blastomycosis (B40.0-B40.2) B40.0 B40.2
  • candidiasis (B37.1) B37.1
  • coccidioidomycosis (B38.0-B38.2) B38.0 B38.2
  • cystic fibrosis with pulmonary manifestations (E84.0) E84.0
  • dermatomyositis (M33.01, M33.11) M33.01 M33.11
  • histoplasmosis (B39.0-B39.2) B39.0 B39.2
  • late syphilis (A52.72, A52.73) A52.72 A52.73
  • polymyositis (M33.21) M33.21
  • Sjögren syndrome (M35.02) M35.02
  • systemic lupus erythematosus (M32.13) M32.13
  • systemic sclerosis (M34.81) M34.81
  • Wegener's granulomatosis (M31.30-M31.31) M31.30 M31.31

Code first

  • underlying disease, such as:
  • amyloidosis (E85.-) E85
  • ankylosing spondylitis (M45.-) M45
  • bronchomycosis (B49) B49
  • congenital syphilis (A50.-) A50
  • cryoglobulinemia (D89.1) D89.1
  • early congenital syphilis (A50.0-) A50.0
  • plasminogen deficiency (E88.02) E88.02
  • schistosomiasis (B65.0-B65.9) B65.0 B65.9

Notes that also apply

Chapter 10 instructions (Notes 1, Excludes2 9, Use additional code 7): printed on the chapter 10 page.

Index entries

  • Bronchomycosis NOS → B49 [J99]
  • Pneumomycosis → B49 [J99]
  • Snuffles (non-syphilitic)syphilitic (infant) → A50.05 [J99]
  • Bilharziasispulmonary NOS → B65.9 [J99]
  • Schistosomiasislung NEC → B65.9 [J99]
  • Schistosomiasispulmonary NEC → B65.9 [J99]
  • Cryoglobulinemia (essential) (idiopathic) (mixed) (primary) (purpura) (secondary) (vasculitis)with lung involvement → D89.1 [J99]
  • Amyloidosis (generalized) (primary)with lung involvement → E85.4 [J99]
  • Amyloidosis (generalized) (primary)pulmonary → E85.4 [J99]
  • Amyloidosis (generalized) (primary)subglottic → E85.4 [J99]
  • Rhinitis (atrophic) (catarrhal) (chronic) (croupous) (fibrinous) (granulomatous) (hyperplastic) (hypertrophic) (membranous) (obstructive) (purulent) (suppurative) (ulcerative)syphiliticcongenital → A50.05 [J99]
  • Laryngitis (acute) (edematous) (fibrinous) (infective) (infiltrative) (malignant) (membranous) (phlegmonous) (pneumococcal) (pseudomembranous) (septic) (subglottic) (suppurative) (ulcerative)syphilitic (late)congenital → A50.59 [J99]
  • Laryngotracheitis (acute) (Infectional) (infective) (viral)syphilitic (late)congenital → A50.59 [J99]
  • Cyst (colloid) (mucous) (simple) (retention)hydatidlung NEC → B67.99 [J99]
  • Spondylitis (chronic)ankylosing (chronic)with lung involvement → M45.9 [J99]
  • Laryngitis (acute) (edematous) (fibrinous) (infective) (infiltrative) (malignant) (membranous) (phlegmonous) (pneumococcal) (pseudomembranous) (septic) (subglottic) (suppurative) (ulcerative)syphilitic (late)congenitalearly → A50.03 [J99]
  • Laryngotracheitis (acute) (Infectional) (infective) (viral)syphilitic (late)congenitalearly → A50.03 [J99]
  • Stenosis, stenotic (cicatricial)larynxsyphiliticcongenital → A50.59 [J99]
  • Stricturelarynxsyphiliticcongenital → A50.59 [J99]
  • Stricturenostril (anterior) (posterior)syphiliticcongenital → A50.59 [J99]
  • Disease, diseasedlunginamyloidosis → E85.4 [J99]

NCHS Alphabetic Index. Index first, then the Tabular List.

Medicare grouping and edits

CMS files for J99
CC / MCCNeither
Appendix BMDC 04 Diseases and Disorders of the Respiratory System, MS-DRG 196-198 (Interstitial Lung Disease with MCC…)
Code EditorManifestation code: not allowed as principal diagnosis
POAReported
HCC V28HCC 280 Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders

CMS: MS-DRG v44 (Appendix B, C), MCE v44, POA list FY2027, 2027 Initial ICD-10-CM Mappings. What the rows mean.

Hierarchy