C88 Malignant immunoproliferative diseases and certain other B-cell lymphomas

Codes in C88

1. C88.0
   Waldenström macroglobulinemia

   Header

   Inclusion terms 2, Excludes1 1

   Inclusion terms

   • Lymphoplasmacytic lymphoma with IgM-production
   • Macroglobulinemia (idiopathic) (primary)

   Excludes1

   • small cell B-cell lymphoma (C83.0) C83.0
2. C88.00
   Waldenström macroglobulinemia not having achieved remission

   Billable21

   Inclusion terms 8

   Inclusion terms

   • Lymphoplasmacytic lymphoma with IgM-production, NOS
   • Lymphoplasmacytic lymphoma with IgM-production not having achieved remission
   • Lymphoplasmacytic lymphoma with IgM-production with failed remission
   • Macroglobulinemia (idiopathic) (primary) NOS
   • Macroglobulinemia (idiopathic) (primary) not having achieved remission
   • Macroglobulinemia (idiopathic) (primary) with failed remission
   • Waldenström macroglobulinemia NOS
   • Waldenström macroglobulinemia with failed remission
3. C88.01
   Waldenström macroglobulinemia, in remission

   Billable21
4. C88.2
   Heavy chain disease

   Header

   Inclusion terms 3

   Inclusion terms

   • Franklin disease
   • Gamma heavy chain disease
   • Mu heavy chain disease
5. C88.20
   Heavy chain disease not having achieved remission

   BillableCC21

   Inclusion terms 11

   Inclusion terms

   • Franklin disease NOS
   • Franklin disease not having achieved remission
   • Franklin disease with failed remission
   • Gamma heavy chain disease NOS
   • Gamma heavy chain disease not having achieved remission
   • Gamma heavy chain disease with failed remission
   • Heavy chain disease NOS
   • Heavy chain disease with failed remissionMu heavy chain disease not having achieved remission
   • Mu heavy chain disease NOS
   • Mu heavy chain disease not having achieved remission
   • Mu heavy chain disease with failed remission
6. C88.21
   Heavy chain disease, in remission

   BillableCC21
7. C88.3
   Immunoproliferative small intestinal disease

   Header

   Inclusion terms 2

   Inclusion terms

   • Alpha heavy chain disease
   • Mediterranean lymphoma
8. C88.30
   Immunoproliferative small intestinal disease not having achieved remission

   BillableCC21

   Inclusion terms 8

   Inclusion terms

   • Alpha heavy chain disease NOS
   • Alpha heavy chain disease not having achieved remission
   • Alpha heavy chain disease with failed remission
   • Immunoproliferative small intestinal disease NOS
   • Immunoproliferative small intestinal disease with failed remission
   • Mediterranean lymphoma NOS
   • Mediterranean lymphoma not having achieved remission
   • Mediterranean lymphoma with failed remission
9. C88.31
   Immunoproliferative small intestinal disease, in remission

   BillableCC21
10. C88.4
    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

    Header

    Inclusion terms 2, Excludes1 1

    Inclusion terms

    • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
    • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]

    Excludes1

    • high malignant (diffuse large B-cell) lymphoma (C83.3-) C83.3
11. C88.40
    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission

    BillableCC21

    Inclusion terms 8

    Inclusion terms

    • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] NOS
    • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] with failed remission
    • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma] NOS
    • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma] not having achieved remission
    • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma] with failed remission
    • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma] NOS
    • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma] not having achieved remission
    • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma] with failed remission
12. C88.41
    Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma], in remission

    BillableCC21
13. C88.8
    Other malignant immunoproliferative diseases

    Header
14. C88.80
    Other malignant immunoproliferative diseases not having achieved remission

    BillableCC21

    Inclusion terms 2

    Inclusion terms

    • Other malignant immunoproliferative diseases NOS
    • Other malignant immunoproliferative diseases with failed remission
15. C88.81
    Other malignant immunoproliferative diseases, in remission

    BillableCC21
16. C88.9
    Malignant immunoproliferative disease, unspecified

    Header

    Inclusion terms 1

    Inclusion terms

    • Immunoproliferative disease NOS
17. C88.90
    Malignant immunoproliferative disease, unspecified not having achieved remission

    BillableCC21

    Inclusion terms 5

    Inclusion terms

    • Immunoproliferative disease NOS
    • Immunoproliferative disease NOS not having achieved remission
    • Immunoproliferative disease NOS with failed remission
    • Malignant immunoproliferative disease, unspecified NOS
    • Malignant immunoproliferative disease, unspecified with failed remission
18. C88.91
    Malignant immunoproliferative disease, unspecified, in remission

    BillableCC21

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

Index entries

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy