DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

C96 Other and unspecified malignant neoplasms of lymphoid, hematopoietic and related tissue

  • Header · not billable

C96 is not billable. The category heads 11 billable codes in FY2027, grouped under 8 subdivisions.

Index → code

  • Letterer-Siwe's disease → C96.0
  • Schüller-Christian disease or syndrome → C96.5
  • Hand-Schüller-Christian disease or syndrome → C96.5

Where it sits

  1. Chapter 2 Neoplasms (C00-D49)
  2. C81-C96 Malignant neoplasms of lymphoid, hematopoietic and related tissue (C81-C96)
  3. C96 Other and unspecified malignant neoplasms of lymphoid, hematopoietic and related tissue
Billable codes
11
Subdivisions
8
CC / MCC codes
11 / 0
HCC V28 codes
11
New FY2027
0
Index entries
45

Codes in C96

  1. C96.0
    Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis
    BillableCC21
    Inclusion terms 2, Excludes1 3

    Inclusion terms

    • Histiocytosis X, multisystemic
    • Letterer-Siwe disease

    Excludes1

    • adult pulmonary Langerhans cell histiocytosis (J84.82) J84.82
    • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5) C96.5
    • unifocal Langerhans-cell histiocytosis (C96.6) C96.6
  2. C96.2
    Malignant mast cell neoplasm
    Header
    Excludes1 3

    Excludes1

    • indolent mastocytosis (D47.02) D47.02
    • mast cell leukemia (C94.30) C94.30
    • mastocytosis (congenital) (cutaneous) (Q82.2) Q82.2
  3. C96.20
    Malignant mast cell neoplasm, unspecified
    BillableCC21
  4. C96.21
    Aggressive systemic mastocytosis
    BillableCC21
  5. C96.22
    Mast cell sarcoma
    BillableCC21
  6. C96.29
    Other malignant mast cell neoplasm
    BillableCC21
  7. C96.4
    Sarcoma of dendritic cells (accessory cells)
    BillableCC21
    Inclusion terms 3

    Inclusion terms

    • Follicular dendritic cell sarcoma
    • Interdigitating dendritic cell sarcoma
    • Langerhans cell sarcoma
  8. C96.5
    Multifocal and unisystemic Langerhans-cell histiocytosis
    BillableCC21
    Inclusion terms 2, Excludes1 2

    Inclusion terms

    • Hand-Schüller-Christian disease
    • Histiocytosis X, multifocal

    Excludes1

    • multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis (C96.0) C96.0
    • unifocal Langerhans-cell histiocytosis (C96.6) C96.6
  9. C96.6
    Unifocal Langerhans-cell histiocytosis
    BillableCC21
    Inclusion terms 4, Excludes1 2

    Inclusion terms

    • Eosinophilic granuloma
    • Histiocytosis X, unifocal
    • Histiocytosis X NOS
    • Langerhans-cell histiocytosis NOS

    Excludes1

    • multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0) C96.0
    • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5) C96.5
  10. C96.A
    Histiocytic sarcoma
    BillableCC21
    Inclusion terms 1

    Inclusion terms

    • Malignant histiocytosis
  11. C96.Z
    Other specified malignant neoplasms of lymphoid, hematopoietic and related tissue
    BillableCC21
  12. C96.9
    Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified
    BillableCC21

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At C96

Excludes1

  • personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79) Z85.79

Notes that also apply

Block C81-C96 instructions (Excludes2 4): printed on the block page.

Chapter 2 instructions (Notes 8): printed on the chapter 2 page.

Index entries

  • Letterer-Siwe's disease → C96.0
  • Hand-Schüller-Christian disease or syndrome → C96.5
  • Schüller-Christian disease or syndrome → C96.5
  • Histiocytosisacute differentiated progressive → C96.0
  • Reticuloendotheliosisacute infantile → C96.0
  • Reticuloendotheliosisnonlipid → C96.0
  • Reticulosis (skin)acute of infancy → C96.0
  • Neoplasm, neoplasticmalignant mast cell → C96.20
  • Mastocytosisaggressive systemic → C96.21
  • Mast cellsarcoma → C96.22
  • Sarcoma (of)mast cell → C96.22
  • Mastocytoma (extracutaneous)malignant → C96.29
  • Mastocytosismalignant → C96.29
  • Sarcoma (of)dendritic cells (accessory cells) → C96.4
  • Sarcoma (of)follicular dendritic cell → C96.4
  • Sarcoma (of)interdigitating dendritic cell → C96.4
  • Sarcoma (of)Langerhans cell → C96.4
  • SyndromeSchüller-Christian → C96.5
  • Xanthoma (s), xanthomatosis (primary) (familial) (hereditary)bone (generalisata) → C96.5
  • Granulomaeosinophilic → C96.6
  • HistiocytosisLangerhans' cell NEC → C96.6
  • HistiocytosisX NEC → C96.6
  • Histiocytosismalignant → C96.A
  • Lymphoma (of) (malignant)true histiocytic → C96.A
  • Reticulosis (skin)histiocytic medullary → C96.A
  • Sarcoma (of)histiocytic → C96.A
  • HistiocytosisX NECacute (progressive) → C96.0
  • HistiocytosisX NECmultisystemic → C96.0
  • Mast cellneoplasmmalignant → C96.20
  • Neoplasm, neoplasticmalignant mast cellspecified type NEC → C96.29
  • HistiocytosisX NECmultifocal → C96.5
  • Granulomaboneeosinophilic → C96.6
  • Granulomabonelung → C96.6
  • Granulomaeosinophilicbone → C96.6
  • Granulomaeosinophiliclung → C96.6
  • Granulomalung (infectious)eosinophilic → C96.6
  • HistiocytosisLangerhans' cell NECunifocal (X) → C96.6
  • Histiocytosismononuclear phagocytes NECLangerhans' cells → C96.6
  • HistiocytosisX NECchronic → C96.6
  • HistiocytosisX NECunifocal → C96.6

5 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy