DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

J84 Other interstitial pulmonary diseases

  • Header · not billable

J84 is not billable. The category heads 24 billable codes in FY2027, grouped under 5 subdivisions.

Index → code

  • Hamman-Rich syndrome → J84.114
  • Lymphangiomyomatosis → J84.81
  • Lymphangioleiomyomatosis → J84.81

Where it sits

  1. Chapter 10 Diseases of the respiratory system (J00-J99)
  2. J80-J84 Other respiratory diseases principally affecting the interstitium (J80-J84)
  3. J84 Other interstitial pulmonary diseases
Billable codes
24
Subdivisions
5
CC / MCC codes
10 / 6
HCC V28 codes
19
New FY2027
0
Index entries
78

Codes in J84

  1. J84.0
    Alveolar and parieto-alveolar conditions
    Header
  2. J84.01
    Alveolar proteinosis
    BillableCC280
  3. J84.02
    Pulmonary alveolar microlithiasis
    BillableCC280
  4. J84.03
    Idiopathic pulmonary hemosiderosis
    BillableCC280
    Inclusion terms 1, Excludes1 1, Code first 2

    Inclusion terms

    • Essential brown induration of lung

    Excludes1

    • acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81) R04.81

    Code first

    • underlying disease, such as:
    • disorders of iron metabolism (E83.1-) E83.1
  5. J84.09
    Other alveolar and parieto-alveolar conditions
    BillableCC280
  6. J84.1
    Other interstitial pulmonary diseases with fibrosis
    Header
    Excludes1 1, Code also 1

    Excludes1

    • pulmonary fibrosis (chronic) following radiation (J70.1) J70.1

    Code also

    • , if applicable, pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4) J68.4
  7. J84.10
    Pulmonary fibrosis, unspecified
    Billable280
    Inclusion terms 5

    Inclusion terms

    • Capillary fibrosis of lung
    • Cirrhosis of lung (chronic) NOS
    • Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
    • Induration of lung (chronic) NOS
    • Postinflammatory pulmonary fibrosis
  8. J84.11
    Idiopathic interstitial pneumonia
    Header
    Excludes1 2

    Excludes1

    • lymphoid interstitial pneumonia (J84.2) J84.2
    • pneumocystis pneumonia (B59) B59
  9. J84.111
    Idiopathic interstitial pneumonia, not otherwise specified
    Billable280
  10. J84.112
    Idiopathic pulmonary fibrosis
    Billable278
    Inclusion terms 2

    Inclusion terms

    • Cryptogenic fibrosing alveolitis
    • Idiopathic fibrosing alveolitis
  11. J84.113
    Idiopathic non-specific interstitial pneumonitis
    Billable280
    Excludes1 1

    Excludes1

    • non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89) J84.89
  12. J84.114
    Acute interstitial pneumonitis
    BillableCC280
    Inclusion terms 1, Excludes1 1

    Inclusion terms

    • Hamman-Rich syndrome

    Excludes1

    • pneumocystis pneumonia (B59) B59
  13. J84.115
    Respiratory bronchiolitis interstitial lung disease
    Billable280
  14. J84.116
    Cryptogenic organizing pneumonia
    BillableCC280
    Excludes1 1

    Excludes1

    • organizing pneumonia NOS, or due to known underlying cause (J84.89) J84.89
  15. J84.117
    Desquamative interstitial pneumonia
    BillableCC280
  16. J84.17
    Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
    Header
  17. J84.170
    Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
    Billable278
    Inclusion terms 1, Code first 5

    Inclusion terms

    • Progressive fibrotic interstitial lung disease

    Code first

    • underlying disease, such as:
    • lung diseases due to external agents (J60-J70) J60 J70
    • rheumatoid arthritis (M05.00-M06.9) M05.00 M06.9
    • sarcoidosis (D86.-) D86
    • systemic connective tissue disorders (M30-M36) M30 M36
  18. J84.178
    Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
    Billable280
    Inclusion terms 4, Code first 4

    Inclusion terms

    • Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
    • Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
    • Organizing pneumonia due to collagen vascular disease
    • Organizing pneumonia in diseases classified elsewhere

    Code first

    • underlying disease, such as:
    • progressive systemic sclerosis (M34.0) M34.0
    • rheumatoid arthritis (M05.00-M06.9) M05.00 M06.9
    • systemic lupus erythematosis (M32.0-M32.9) M32.0 M32.9
  19. J84.2
    Lymphoid interstitial pneumonia
    BillableCC280
    Inclusion terms 1

    Inclusion terms

    • Lymphoid interstitial pneumonitis
  20. J84.8
    Other specified interstitial pulmonary diseases
    Header
    Excludes1 2

    Excludes1

    • exogenous lipoid pneumonia (J69.1) J69.1
    • unspecified lipoid pneumonia (J69.1) J69.1
  21. J84.81
    Lymphangioleiomyomatosis
    BillableMCC280
    Inclusion terms 1

    Inclusion terms

    • Lymphangiomyomatosis
  22. J84.82
    Adult pulmonary Langerhans cell histiocytosis
    BillableCC280
    Inclusion terms 1

    Inclusion terms

    • Adult PLCH
  23. J84.83
    Surfactant mutations of the lung
    BillableMCC
  24. J84.84
    Other interstitial lung diseases of childhood
    Header
  25. J84.841
    Neuroendocrine cell hyperplasia of infancy
    BillableMCC
  26. J84.842
    Pulmonary interstitial glycogenosis
    BillableMCC
  27. J84.843
    Alveolar capillary dysplasia with vein misalignment
    BillableMCC
  28. J84.848
    Other interstitial lung diseases of childhood
    BillableMCC
  29. J84.89
    Other specified interstitial pulmonary diseases
    Billable280
    Inclusion terms 4, Excludes1 4, Code first 3, Use additional code 1

    Inclusion terms

    • Endogenous lipoid pneumonia
    • Interstitial pneumonitis
    • Non-specific interstitial pneumonitis NOS
    • Organizing pneumonia NOS

    Excludes1

    • cryptogenic organizing pneumonia (J84.116) J84.116
    • idiopathic non-specific interstitial pneumonitis (J84.113) J84.113
    • lipoid pneumonia, exogenous or unspecified (J69.1) J69.1
    • lymphoid interstitial pneumonia (J84.2) J84.2

    Code first

    • , if applicable:
    • poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy T51 T65
    • underlying cause of pneumonopathy, if known

    Use additional code

    • code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced T36 T50
  30. J84.9
    Interstitial pulmonary disease, unspecified
    BillableCC280
    Inclusion terms 1

    Inclusion terms

    • Interstitial pneumonia NOS

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At J84

Excludes1

  • drug-induced interstitial lung disorders (J70.2-J70.4) J70.2 J70.4
  • interstitial emphysema (J98.2) J98.2

Excludes2

  • lung diseases due to external agents (J60-J70) J60 J70

Code also

  • , if applicable, associated condition

Notes that also apply

Chapter 10 instructions (Notes 1, Excludes2 9, Use additional code 7): printed on the chapter 10 page.

Index entries

  • Microlithiasis, alveolar, pulmonary → J84.02
  • Hamman-Rich syndrome → J84.114
  • Lymphangioleiomyomatosis → J84.81
  • Lymphangiomyomatosis → J84.81
  • BOOP (bronchiolitis obliterans organized pneumonia) → J84.89
  • Hemosiderosis (dietary)pulmonary, idiopathic → E83.1- [J84.03]
  • Proteinosisalveolar (pulmonary) → J84.01
  • Disorder (of)alveolar NEC → J84.09
  • Disorder (of)parietoalveolar NEC → J84.09
  • Pneumopathy NECalveolar → J84.09
  • Pneumopathy NECparietoalveolar → J84.09
  • Block, blockedalveolocapillary → J84.10
  • Cirrhosis, cirrhotic (hepatic) (liver)lung (chronic) → J84.10
  • Cirrhosis, cirrhotic (hepatic) (liver)pulmonary → J84.10
  • Fibrosis, fibroticlung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) → J84.10
  • Fibrosis, fibroticpulmonary → J84.10
  • Induration, induratedlung (black) (chronic) (fibroid) → J84.10
  • Syndromealveolocapillary block → J84.10
  • Alveolitisfibrosing (cryptogenic) (idiopathic) → J84.112
  • Bronchiolitis (acute) (infective) (subacute)respiratory, interstitial lung disease → J84.115
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)cryptogenic organizing → J84.116
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)desquamative interstitial → J84.117
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)lymphoid interstitial → J84.2
  • Pneumonitis (acute) (primary)lymphoid, interstitial → J84.2
  • Mutation(s)surfactant, of lung → J84.83
  • Hyperplasia, hyperplasticneuroendocrine cell, of infancy → J84.841
  • Glycogenosis (diffuse) (generalized)pulmonary interstitial → J84.842
  • Dysplasiaalveolar capillary, with vein misalignment → J84.843
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)bronchiolitis obliterans organized (BOOP) → J84.89
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)cholesterol → J84.89
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)organizing → J84.89
  • Pneumonitis (acute) (primary)cholesterol → J84.89
  • Pneumonitis (acute) (primary)interstitial (chronic) → J84.89
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)interstitial → J84.9
  • Induration, induratedlung (black) (chronic) (fibroid)essential brown → J84.03
  • Fibrosis, fibroticlung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial)capillary → J84.10
  • Fibrosis, fibroticlung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial)diffuse (idiopathic) → J84.10
  • Fibrosis, fibroticlung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial)postinflammatory → J84.10
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)interstitialchronic → J84.111
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)interstitialidiopathic NOS → J84.111

38 more, longer entries are not listed; the search box finds them by word.

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