DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q82 Other congenital malformations of skin

  • Header · not billable

Q82 is not billable. The category heads 9 billable codes in FY2027: the 9 codes directly below it.

Index → code

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q80-Q89 Other congenital malformations (Q80-Q89)
  3. Q82 Other congenital malformations of skin
Billable codes
9
Subdivisions
9
CC / MCC codes
0 / 0
HCC V28 codes
0
New FY2027
0
Index entries
120

Codes in Q82

  1. Q82.0
    Hereditary lymphedema
    BillableExempt
  2. Q82.1
    Xeroderma pigmentosum
    BillableExempt
  3. Q82.2
    Congenital cutaneous mastocytosis
    BillableExempt
    Inclusion terms 3, Excludes1 5

    Inclusion terms

    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa

    Excludes1

    • cutaneous mastocytosis NOS (D47.01) D47.01
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01) D47.01
    • malignant mastocytosis (C96.2-) C96.2
    • systemic mastocytosis (D47.02) D47.02
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01) D47.01
  4. Q82.3
    Incontinentia pigmenti
    BillableExempt
  5. Q82.4
    Ectodermal dysplasia (anhidrotic)
    BillableExempt
    Excludes1 1

    Excludes1

    • Ellis-van Creveld syndrome (Q77.6) Q77.6
  6. Q82.5
    Congenital non-neoplastic nevus
    BillableExempt
    Inclusion terms 7, Excludes2 8

    Inclusion terms

    • Birthmark NOS
    • Flammeus Nevus
    • Portwine Nevus
    • Sanguineous Nevus
    • Strawberry Nevus
    • Vascular Nevus NOS
    • Verrucous Nevus

    Excludes2

    • Café au lait spots (L81.3) L81.3
    • lentigo (L81.4) L81.4
    • nevus NOS (D22.-) D22
    • araneus nevus (I78.1) I78.1
    • melanocytic nevus (D22.-) D22
    • pigmented nevus (D22.-) D22
    • spider nevus (I78.1) I78.1
    • stellar nevus (I78.1) I78.1
  7. Q82.6
    Congenital sacral dimple
    BillableExempt
    Inclusion terms 1, Excludes2 2

    Inclusion terms

    • Parasacral dimple

    Excludes2

    • pilonidal cyst with abscess (L05.01) L05.01
    • pilonidal cyst without abscess (L05.91) L05.91
  8. Q82.8
    Other specified congenital malformations of skin
    BillableExempt
    Inclusion terms 8, Excludes1 1, Excludes2 1

    Inclusion terms

    • Abnormal palmar creases
    • Accessory skin tags
    • Benign familial pemphigus [Hailey-Hailey]
    • Congenital poikiloderma
    • Cutis laxa (hyperelastica)
    • Dermatoglyphic anomalies
    • Inherited keratosis palmaris et plantaris
    • Keratosis follicularis [Darier-White]

    Excludes1

    • Ehlers-Danlos syndromes (Q79.6-) Q79.6

    Excludes2

    • disorders of pyrophosphate metabolism (E83.82-) E83.82
  9. Q82.9
    Congenital malformation of skin, unspecified
    BillableExempt

Sources of each column.

Instructions

At Q82

Excludes1

  • acrodermatitis enteropathica (E83.2) E83.2
  • congenital erythropoietic porphyria (E80.0) E80.0
  • pilonidal cyst or sinus (L05.-) L05
  • Sturge-Weber (-Dimitri) syndrome (Q85.89) Q85.89

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Meige-Milroy disease (chronic hereditary edema) → Q82.0
  • Meige's syndrome → Q82.0
  • Milroy's disease (chronic hereditary edema) → Q82.0
  • Nonne-Milroy syndrome → Q82.0
  • Pseudoelephantiasis neuroarthritica → Q82.0
  • Trophedema (congenital) (hereditary) → Q82.0
  • Tropholymphedema → Q82.0
  • Epitheliomatosis pigmented → Q82.1
  • Bloch-Sulzberger disease or syndrome → Q82.3
  • Incontinentia pigmenti → Q82.3
  • Basan's (hidrotic) ectodermal dysplasia → Q82.4
  • Bason's (hidrotic) ectodermal dysplasia → Q82.4
  • Clouston's (hidrotic) ectodermal dysplasia → Q82.4
  • Ectodermal dysplasia (anhidrotic) → Q82.4
  • Feinmesser's (hidrotic) ectodermal dysplasia → Q82.4
  • Marshall's (hidrotic) ectodermal dysplasia → Q82.4
  • Robinson's (hidrotic) ectodermal dysplasia or syndrome → Q82.4
  • Birthmark → Q82.5
  • Port wine nevus, mark, or stain → Q82.5
  • Angiomatosis → Q82.8
  • Bloom (-Machacek)(-Torre) syndrome → Q82.8
  • Brugsch's syndrome → Q82.8
  • Darier (-White) disease (congenital) → Q82.8
  • Dermatolysis (exfoliativa) (congenital) → Q82.8
  • Dermatomegaly NEC → Q82.8
  • Elastic skin → Q82.8
  • Elastoma (juvenile) → Q82.8
  • Gyrate scalp → Q82.8
  • Hailey-Hailey disease → Q82.8
  • India rubber skin → Q82.8
  • Keratoderma, keratodermia (congenital) (palmaris et plantaris) (symmetrical) → Q82.8
  • Melanocytosis, neurocutaneous → Q82.8
  • Mibelli's disease (porokeratosis) → Q82.8
  • Pachydermatocele (congenital) → Q82.8
  • Particolored infant → Q82.8
  • Porokeratosis → Q82.8
  • Pseudoxanthoma elasticum → Q82.8
  • Rothmund (-Thomson) syndrome → Q82.8
  • Siemens' syndrome (ectodermal dysplasia) → Q82.8
  • Disease, diseasedMeige's (chronic hereditary edema) → Q82.0

80 more, longer entries are not listed; the search box finds them by word.

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