DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q80 Congenital ichthyosis

  • Header · not billable

Q80 is not billable. The category heads 7 billable codes in FY2027: the 7 codes directly below it.

Index → code

  • Collodion baby → Q80.2
  • Harlequin (newborn) → Q80.4
  • Alligator skin disease → Q80.9
Billable codes
7
Subdivisions
7
CC / MCC codes
0 / 0
HCC V28 codes
0
New FY2027
0
Index entries
18

Codes in Q80

  1. Q80.0
    Ichthyosis vulgaris
    BillableExempt
  2. Q80.1
    X-linked ichthyosis
    BillableExempt
  3. Q80.2
    Lamellar ichthyosis
    BillableExempt
    Inclusion terms 1

    Inclusion terms

    • Collodion baby
  4. Q80.3
    Congenital bullous ichthyosiform erythroderma
    BillableExempt
  5. Q80.4
    Harlequin fetus
    BillableExempt
  6. Q80.8
    Other congenital ichthyosis
    BillableExempt
  7. Q80.9
    Congenital ichthyosis, unspecified
    BillableExempt

Sources of each column.

Instructions

At Q80

Excludes1

  • Refsum's disease (G60.1) G60.1

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Collodion baby → Q80.2
  • Harlequin (newborn) → Q80.4
  • Alligator skin disease → Q80.9
  • Ichthyosis (congenital) → Q80.9
  • Ichthyosis (congenital)simplex → Q80.0
  • Ichthyosis (congenital)vulgaris → Q80.0
  • Ichthyosis (congenital)X-linked → Q80.1
  • Ichthyosis (congenital)lamellar → Q80.2
  • Erythema, erythematous (infectional) (inflammation)ichthyosiforme congenitum bullous → Q80.3
  • Erythroderma (secondary)bullous ichthyosiform, congenital → Q80.3
  • Erythroderma (secondary)ichthyosiform, congenital (bullous) → Q80.3
  • Ichthyosis (congenital)fetalis → Q80.4
  • Hyperkeratosisuniversalis congenita → Q80.8
  • Ichthyosis (congenital)hystrix → Q80.8
  • Ichthyosis (congenital)vera → Q80.8
  • Keratosiscongenital, specified NEC → Q80.8
  • Disease, diseasedalligator-skin → Q80.9
  • Disease, diseasedfish-skin → Q80.9

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy