DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

  • Header · not billable

D76 is not billable. The category heads 3 billable codes in FY2027: the 3 codes directly below it.

Index → code

  • Histiocytosis → D76.3
  • Xanthogranuloma → D76.3
  • Reticulohistiocytoma (giant-cell) → D76.3

Where it sits

  1. Chapter 3 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
  2. D70-D77 Other disorders of blood and blood-forming organs (D70-D77)
  3. D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
Billable codes
3
Subdivisions
3
CC / MCC codes
3 / 0
HCC V28 codes
2
New FY2027
0
Index entries
18

Codes in D76

  1. D76.1
    Hemophagocytic lymphohistiocytosis
    BillableCC115
    Inclusion terms 2

    Inclusion terms

    • Familial hemophagocytic reticulosis
    • Histiocytoses of mononuclear phagocytes
  2. D76.2
    Hemophagocytic syndrome, infection-associated
    BillableCC
    Use additional code 1

    Use additional code

    • code to identify infectious agent or disease.
  3. D76.3
    Other histiocytosis syndromes
    BillableCC115
    Inclusion terms 3

    Inclusion terms

    • Reticulohistiocytoma (giant-cell)
    • Sinus histiocytosis with massive lymphadenopathy
    • Xanthogranuloma

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At D76

Excludes1

  • (Abt-) Letterer-Siwe disease (C96.0) C96.0
  • eosinophilic granuloma (C96.6) C96.6
  • Hand-Schüller-Christian disease (C96.5) C96.5
  • histiocytic medullary reticulosis (C96.9) C96.9
  • histiocytic sarcoma (C96.A) C96.A
  • histiocytosis X, multifocal (C96.5) C96.5
  • histiocytosis X, unifocal (C96.6) C96.6
  • Langerhans-cell histiocytosis, multifocal (C96.5) C96.5
  • Langerhans-cell histiocytosis NOS (C96.6) C96.6
  • Langerhans-cell histiocytosis, unifocal (C96.6) C96.6
  • leukemic reticuloendotheliosis (C91.4-) C91.4
  • lipomelanotic reticulosis (I89.8) I89.8
  • malignant histiocytosis (C96.A) C96.A
  • malignant reticulosis (C86.0) C86.0
  • nonlipid reticuloendotheliosis (C96.0) C96.0

Notes that also apply

Chapter 3 instructions (Excludes2 9): printed on the chapter 3 page.

Index entries

  • Lymphohistiocytosis, hemophagocytic (familial) → D76.1
  • Histiocytosis → D76.3
  • Reticulohistiocytoma (giant-cell) → D76.3
  • Xanthogranuloma → D76.3
  • Histiocytosismononuclear phagocytes NEC → D76.1
  • Reticulosis (skin)hemophagocytic, familial → D76.1
  • Syndromemacrophage activation → D76.1
  • Syndromehemophagocytic, infection-associated → D76.2
  • Granulomareticulohistiocytic → D76.3
  • Histiocytosislipid, lipoid → D76.3
  • Histiocytosisnon-Langerhans cell → D76.3
  • Histiocytosispolyostotic sclerosing → D76.3
  • Histiocytosissinus, with massive lymphadenopathy → D76.3
  • Histiocytosissyndrome NEC → D76.3
  • Lipoidhistiocytosis → D76.3
  • Syndromehistiocytic → D76.3
  • Syndromehistiocytosis NEC → D76.3
  • Syndromemacrophage activationdue to infection → D76.2

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy