DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

G11 Hereditary ataxia

  • Header · not billable

G11 is not billable. The category heads 11 billable codes in FY2027, grouped under 9 subdivisions.

Index → code

  • Sanger-Brown ataxia → G11.2
  • Ataxia-telangiectasia (Louis-Bar) → G11.3
  • Louis-Bar syndrome (ataxia-telangiectasia) → G11.3

Where it sits

  1. Chapter 6 Diseases of the nervous system (G00-G99)
  2. G10-G14 Systemic atrophies primarily affecting the central nervous system (G10-G14)
  3. G11 Hereditary ataxia
Billable codes
11
Subdivisions
9
CC / MCC codes
11 / 0
HCC V28 codes
11
New FY2027
0
Index entries
63

Codes in G11

  1. G11.0
    Congenital nonprogressive ataxia
    BillableCC200
  2. G11.1
    Early-onset cerebellar ataxia
    Header
  3. G11.10
    Early-onset cerebellar ataxia, unspecified
    BillableCC200
  4. G11.11
    Friedreich ataxia
    BillableCC200
    Inclusion terms 2

    Inclusion terms

    • Autosomal recessive Friedreich ataxia
    • Friedreich ataxia with retained reflexes
  5. G11.19
    Other early-onset cerebellar ataxia
    BillableCC200
    Inclusion terms 4

    Inclusion terms

    • Early-onset cerebellar ataxia with essential tremor
    • Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia]
    • Early-onset cerebellar ataxia with retained tendon reflexes
    • X-linked recessive spinocerebellar ataxia
  6. G11.2
    Late-onset cerebellar ataxia
    BillableCC200
  7. G11.3
    Cerebellar ataxia with defective DNA repair
    BillableCC200
    Inclusion terms 1, Excludes2 3

    Inclusion terms

    • Ataxia telangiectasia [Louis-Bar]

    Excludes2

    • Cockayne's syndrome (Q87.19) Q87.19
    • other disorders of purine and pyrimidine metabolism (E79.-) E79
    • xeroderma pigmentosum (Q82.1) Q82.1
  8. G11.4
    Hereditary spastic paraplegia
    BillableCC200
  9. G11.5
    Hypomyelination - hypogonadotropic hypogonadism - hypodontia
    BillableCC200
    Inclusion terms 2

    Inclusion terms

    • 4H syndrome
    • Pol III-related leukodystrophy
  10. G11.6
    Leukodystrophy with vanishing white matter disease
    BillableCC200
  11. G11.8
    Other hereditary ataxias
    BillableCC200
  12. G11.9
    Hereditary ataxia, unspecified
    BillableCC200
    Inclusion terms 4

    Inclusion terms

    • Hereditary cerebellar ataxia NOS
    • Hereditary cerebellar degeneration
    • Hereditary cerebellar disease
    • Hereditary cerebellar syndrome

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At G11

Excludes2

  • cerebral palsy (G80.-) G80
  • hereditary and idiopathic neuropathy (G60.-) G60
  • metabolic disorders (E70-E88) E70 E88

Notes that also apply

Chapter 6 instructions (Excludes2 8): printed on the chapter 6 page.

Index entries

  • Sanger-Brown ataxia → G11.2
  • Ataxia-telangiectasia (Louis-Bar) → G11.3
  • Boder-Sedgwick syndrome (ataxia-telangiectasia) → G11.3
  • Louis-Bar syndrome (ataxia-telangiectasia) → G11.3
  • Hypomyelination - hypogonadotropic hypogonadism - hypodontia → G11.5
  • Ataxia, ataxy, ataxiccongenital nonprogressive → G11.0
  • Ataxia, ataxy, ataxicnonprogressive, congenital → G11.0
  • Ataxia, ataxy, ataxicautosomal recessive Friedreich → G11.11
  • Ataxia, ataxy, ataxicFriedreich's (heredofamilial) (cerebellar) (spinal) (with retained reflexes) → G11.11
  • Friedreich'sataxia → G11.11
  • Friedreich'scombined systemic disease → G11.11
  • Friedreich'ssclerosis (cerebellum) (spinal cord) → G11.11
  • Sclerosis, scleroticFriedreich's (spinal cord) → G11.11
  • Ataxia, ataxy, ataxicHunt's → G11.19
  • Ataxia, ataxy, ataxicspinocerebellar, X-linked recessive → G11.19
  • Dyssynergiacerebellaris myoclonica (Hunt's ataxia) → G11.19
  • Ramsay-Hunt disease or syndromemeaning dyssynergia cerebellaris myoclonica → G11.19
  • Ataxia, ataxy, ataxicMarie's (cerebellar) (heredofamilial) (late- onset) → G11.2
  • Ataxia, ataxy, ataxicSanger-Brown's (hereditary) → G11.2
  • Marie'scerebellar ataxia (late-onset) → G11.2
  • Ataxia, ataxy, ataxictelangiectasia (Louis-Bar) → G11.3
  • Syndromeataxia-telangiectasia → G11.3
  • SyndromeBoder-Sedgewick → G11.3
  • SyndromeLouis-Barré → G11.3
  • Telangiectasia, telangiectasis (verrucous)ataxic (cerebellar) (Louis-Bar) → G11.3
  • Ataxia, ataxy, ataxicspastic hereditary → G11.4
  • Paraplegia (lower)familial spastic → G11.4
  • Paraplegia (lower)hereditary, spastic → G11.4
  • Leukodystrophypol III-related → G11.5
  • Syndrome4H → G11.5
  • Leukodystrophywith vanishing white matter disease → G11.6
  • Ataxia, ataxy, ataxicbrain (hereditary) → G11.9
  • Ataxia, ataxy, ataxiccerebellar (hereditary) → G11.9
  • Ataxia, ataxy, ataxiccerebral (hereditary) → G11.9
  • Ataxia, ataxy, ataxichereditary → G11.9
  • Disease, diseasedspinocerebellar (hereditary) → G11.9
  • Paralysis, paralytic (complete) (incomplete)ataxic (hereditary) → G11.9
  • Ataxia, ataxy, ataxiccerebellar (hereditary)early-onset → G11.10
  • Ataxia, ataxy, ataxichereditaryspinal (Friedreich's) → G11.11
  • Ataxia, ataxy, ataxicspinalhereditary (Friedreich's) → G11.11

23 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy