DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q25 Congenital malformations of great arteries

  • Header · not billable

Q25 is not billable. The category heads 22 billable codes in FY2027, grouped under 10 subdivisions.

Index → code

  • Right aortic arch → Q25.47
  • Pseudotruncus arteriosus → Q25.49
  • Botalli, ductus (patent) (persistent) → Q25.0

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q20-Q28 Congenital malformations of the circulatory system (Q20-Q28)
  3. Q25 Congenital malformations of great arteries
Billable codes
22
Subdivisions
10
CC / MCC codes
17 / 5
HCC V28 codes
0
New FY2027
0
Index entries
103

Codes in Q25

  1. Q25.0
    Patent ductus arteriosus
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Patent ductus Botallo
    • Persistent ductus arteriosus
  2. Q25.1
    Coarctation of aorta
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Coarctation of aorta (preductal) (postductal)
    • Stenosis of aorta
  3. Q25.2
    Atresia of aorta
    Header
  4. Q25.21
    Interruption of aortic arch
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Atresia of aortic arch
  5. Q25.29
    Other atresia of aorta
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Atresia of aorta
  6. Q25.3
    Supravalvular aortic stenosis
    BillableCCExempt
    Excludes1 2

    Excludes1

    • congenital aortic stenosis NOS (Q23.0) Q23.0
    • congenital stenosis of aortic valve (Q23.0) Q23.0
  7. Q25.4
    Other congenital malformations of aorta
    Header
    Excludes1 1

    Excludes1

    • hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4) Q23.4
  8. Q25.40
    Congenital malformation of aorta unspecified
    BillableCCExempt
  9. Q25.41
    Absence and aplasia of aorta
    BillableCCExempt
  10. Q25.42
    Hypoplasia of aorta
    BillableCCExempt
  11. Q25.43
    Congenital aneurysm of aorta
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Congenital aneurysm of aortic root
    • Congenital aneurysm of aortic sinus
  12. Q25.44
    Congenital dilation of aorta
    BillableCCExempt
  13. Q25.45
    Double aortic arch
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Vascular ring of aorta
  14. Q25.46
    Tortuous aortic arch
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Persistent convolutions of aortic arch
  15. Q25.47
    Right aortic arch
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Persistent right aortic arch
  16. Q25.48
    Anomalous origin of subclavian artery
    BillableCCExempt
  17. Q25.49
    Other congenital malformations of aorta
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Aortic arch
    • Bovine arch
  18. Q25.5
    Atresia of pulmonary artery
    BillableMCCExempt
  19. Q25.6
    Stenosis of pulmonary artery
    BillableMCCExempt
    Inclusion terms 1

    Inclusion terms

    • Supravalvular pulmonary stenosis
  20. Q25.7
    Other congenital malformations of pulmonary artery
    Header
  21. Q25.71
    Coarctation of pulmonary artery
    BillableMCCExempt
  22. Q25.72
    Congenital pulmonary arteriovenous malformation
    BillableMCCExempt
    Inclusion terms 1

    Inclusion terms

    • Congenital pulmonary arteriovenous aneurysm
  23. Q25.79
    Other congenital malformations of pulmonary artery
    BillableMCCExempt
    Inclusion terms 5

    Inclusion terms

    • Aberrant pulmonary artery
    • Agenesis of pulmonary artery
    • Congenital aneurysm of pulmonary artery
    • Congenital anomaly of pulmonary artery
    • Hypoplasia of pulmonary artery
  24. Q25.8
    Other congenital malformations of other great arteries
    BillableCCExempt
  25. Q25.9
    Congenital malformation of great arteries, unspecified
    BillableCCExempt

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Botalli, ductus (patent) (persistent) → Q25.0
  • Right aortic arch → Q25.47
  • Pseudotruncus arteriosus → Q25.49
  • Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)ductus arteriosus → Q25.0
  • Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)patent ductus arteriosus → Q25.0
  • Deformityductus arteriosus → Q25.0
  • Nonclosureductus arteriosus (Botallo's) → Q25.0
  • Patentductus arteriosus or Botallo's → Q25.0
  • Persistence, persistent (congenital)ductus arteriosus (Botalli) → Q25.0
  • Pervious, congenitalductus arteriosus → Q25.0
  • Coarctationaorta (preductal) (postductal) → Q25.1
  • Stenosis, stenotic (cicatricial)aorta (ascending) (supraventricular) (congenital) → Q25.1
  • Strictureaorta (ascending) (congenital) → Q25.1
  • Interruptionaortic arch → Q25.21
  • Atresia, atreticaorta (ring) → Q25.29
  • Anomaly, anomalous (congenital) (unspecified type)aorta (arch) NEC → Q25.40
  • Deformityaorta (arch) (congenital) → Q25.40
  • Malformation (congenital)aorta → Q25.40
  • Absence (of) (organ or part) (complete or partial)aorta (congenital) → Q25.41
  • Agenesisaorta → Q25.41
  • Aplasiaaorta (congenital) → Q25.41
  • Hypoplasia, hypoplasticaorta, aortic → Q25.42
  • Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)sinus of Valsalva → Q25.43
  • Doubleaortic arch → Q25.45
  • Persistence, persistent (congenital)double aortic arch → Q25.45
  • Ring(s)aorta (vascular) → Q25.45
  • Tortuousaortic arch → Q25.46
  • Persistence, persistent (congenital)right aortic arch → Q25.47
  • Absence (of) (organ or part) (complete or partial)transverse aortic arch, congenital → Q25.49
  • Anomaly, anomalous (congenital) (unspecified type)sinus of Valsalva → Q25.49
  • Archaortic → Q25.49
  • Archbovine → Q25.49
  • Congenitalaortic septum → Q25.49
  • Deformitytransverse aortic arch (congenital) → Q25.49
  • Overridingaorta → Q25.49
  • Atresia, atreticpulmonary (artery) → Q25.5
  • Stenosis, stenotic (cicatricial)pulmonary (artery) (congenital) → Q25.6
  • Coarctationpulmonary artery → Q25.71
  • Ring(s)vascular (congenital) → Q25.8
  • Anomaly, anomalous (congenital) (unspecified type)ductusarteriosus → Q25.0

63 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

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