DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q26 Congenital malformations of great veins

  • Header · not billable

Q26 is not billable. The category heads 9 billable codes in FY2027: the 9 codes directly below it.

Index → code

  • Scimitar syndrome → Q26.8
  • Syndromescimitar → Q26.8
  • Azygoscontinuation inferior vena cava → Q26.8

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q20-Q28 Congenital malformations of the circulatory system (Q20-Q28)
  3. Q26 Congenital malformations of great veins
Billable codes
9
Subdivisions
9
CC / MCC codes
7 / 0
HCC V28 codes
0
New FY2027
0
Index entries
52

Codes in Q26

  1. Q26.0
    Congenital stenosis of vena cava
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Congenital stenosis of vena cava (inferior)(superior)
  2. Q26.1
    Persistent left superior vena cava
    BillableCCExempt
  3. Q26.2
    Total anomalous pulmonary venous connection
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic
    • Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic
  4. Q26.3
    Partial anomalous pulmonary venous connection
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Partial anomalous pulmonary venous return
  5. Q26.4
    Anomalous pulmonary venous connection, unspecified
    BillableCCExempt
  6. Q26.5
    Anomalous portal venous connection
    BillableExempt
  7. Q26.6
    Portal vein-hepatic artery fistula
    BillableExempt
  8. Q26.8
    Other congenital malformations of great veins
    BillableCCExempt
    Inclusion terms 4

    Inclusion terms

    • Absence of vena cava (inferior) (superior)
    • Azygos continuation of inferior vena cava
    • Persistent left posterior cardinal vein
    • Scimitar syndrome
  9. Q26.9
    Congenital malformation of great vein, unspecified
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Congenital anomaly of vena cava (inferior) (superior) NOS

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Scimitar syndrome → Q26.8
  • Anomaly, anomalous (congenital) (unspecified type)opening, pulmonary veins → Q26.4
  • Anomaly, anomalous (congenital) (unspecified type)portal vein → Q26.5
  • Fistula (cutaneous)hepatic artery-portal vein, congenital → Q26.6
  • Fistula (cutaneous)portal vein-hepatic artery, congenital → Q26.6
  • Absence (of) (organ or part) (complete or partial)superior vena cava, congenital → Q26.8
  • Absence (of) (organ or part) (complete or partial)vena cava (inferior) (superior), congenital → Q26.8
  • Agenesisvena cava (inferior) (superior) → Q26.8
  • Anomaly, anomalous (congenital) (unspecified type)venous return → Q26.8
  • Atresia, atreticvena cava (inferior) (superior) → Q26.8
  • Azygoscontinuation inferior vena cava → Q26.8
  • Hypoplasia, hypoplasticvena cava (inferior) (superior) → Q26.8
  • Syndromescimitar → Q26.8
  • Anomaly, anomalous (congenital) (unspecified type)vena cava (inferior) (superior) → Q26.9
  • Stenosis, stenotic (cicatricial)vena cava (inferior) (superior)congenital → Q26.0
  • Stricturevena cava (inferior) (superior) NECcongenital → Q26.0
  • Persistence, persistent (congenital)leftsuperior vena cava → Q26.1
  • Terminationanomalousright pulmonary vein → Q26.3
  • Anomaly, anomalous (congenital) (unspecified type)connectionpulmonary venous → Q26.4
  • Anomaly, anomalous (congenital) (unspecified type)pulmonaryvenous connection → Q26.4
  • Atresia, atreticvein NECpulmonary → Q26.4
  • Absence (of) (organ or part) (complete or partial)vein (peripheral) congenital NECportal → Q26.5
  • Agenesisvein(s) (peripheral)portal → Q26.5
  • Anomaly, anomalous (congenital) (unspecified type)connectionportal vein → Q26.5
  • Anomaly, anomalous (congenital) (unspecified type)portal veinconnection → Q26.5
  • Atresia, atreticvein NECportal → Q26.5
  • Absence (of) (organ or part) (complete or partial)vein (peripheral) congenital NECgreat → Q26.8
  • Agenesisvein(s) (peripheral)great NEC → Q26.8
  • Atresia, atreticvein NECgreat → Q26.8
  • Hypoplasia, hypoplasticvein(s) (peripheral)great → Q26.8
  • Malpositioncongenitalvena cava (inferior) (superior) → Q26.8
  • Persistence, persistent (congenital)leftposterior cardinal vein → Q26.8
  • Persistence, persistent (congenital)sinusvenosus with imperfect incorporation in right auricle → Q26.8
  • Anomaly, anomalous (congenital) (unspecified type)vein(s) (peripheral)great → Q26.9
  • Deformityvein (congenital)great → Q26.9
  • Malformation (congenital)greatvein → Q26.9
  • Malformation (congenital)greatveinvena cava stenosis, congenital → Q26.0
  • Malformation (congenital)greatveinpersistent left superior vena cava → Q26.1
  • Anomaly, anomalous (congenital) (unspecified type)connectionpulmonary venoustotal → Q26.2
  • Anomaly, anomalous (congenital) (unspecified type)pulmonaryvenous connectiontotal → Q26.2

12 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy