DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q78 Other osteochondrodysplasias

  • Header · not billable

Q78 is not billable. The category heads 9 billable codes in FY2027: the 9 codes directly below it.

Index → code

Billable codes
9
Subdivisions
9
CC / MCC codes
2 / 0
HCC V28 codes
0
New FY2027
0
Index entries
83

Codes in Q78

  1. Q78.0
    Osteogenesis imperfecta
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Fragilitas ossium
    • Osteopsathyrosis
  2. Q78.1
    Polyostotic fibrous dysplasia
    BillableExempt
    Inclusion terms 1

    Inclusion terms

    • Albright(-McCune)(-Sternberg) syndrome
  3. Q78.2
    Osteopetrosis
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Albers-Schönberg syndrome
    • Osteosclerosis NOS
  4. Q78.3
    Progressive diaphyseal dysplasia
    BillableExempt
    Inclusion terms 1

    Inclusion terms

    • Camurati-Engelmann syndrome
  5. Q78.4
    Enchondromatosis
    BillableExempt
    Inclusion terms 2

    Inclusion terms

    • Maffucci's syndrome
    • Ollier's disease
  6. Q78.5
    Metaphyseal dysplasia
    BillableExempt
    Inclusion terms 1

    Inclusion terms

    • Pyle's syndrome
  7. Q78.6
    Multiple congenital exostoses
    BillableExempt
    Inclusion terms 1

    Inclusion terms

    • Diaphyseal aclasis
  8. Q78.8
    Other specified osteochondrodysplasias
    BillableExempt
    Inclusion terms 1

    Inclusion terms

    • Osteopoikilosis
  9. Q78.9
    Osteochondrodysplasia, unspecified
    BillableExempt
    Inclusion terms 2

    Inclusion terms

    • Chondrodystrophy NOS
    • Osteodystrophy NOS

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At Q78

Excludes2

  • congenital myotonic chondrodystrophy (G71.13) G71.13

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Adair-Dighton syndrome (brittle bones and blue sclera, deafness) → Q78.0
  • Eddowes (-Spurway) syndrome → Q78.0
  • Ekman's syndrome (brittle bones and blue sclera) → Q78.0
  • Lobstein (-Ekman) disease or syndrome → Q78.0
  • Osteogenesis imperfecta → Q78.0
  • Osteopsathyrosis (idiopathica) → Q78.0
  • Spurway's syndrome → Q78.0
  • Van der Hoeve (-de Kleyn) syndrome → Q78.0
  • Vrolik's disease → Q78.0
  • Albright (-McCune)(-Sternberg) syndrome → Q78.1
  • McCune-Albright syndrome → Q78.1
  • Polyostotic fibrous dysplasia → Q78.1
  • Albers-Schönberg syndrome → Q78.2
  • Ivory bones → Q78.2
  • Osteopetrosis (familial) → Q78.2
  • Osteosclerosis → Q78.2
  • Camurati-Engelmann syndrome → Q78.3
  • Engelmann (-Camurati) syndrome → Q78.3
  • Dyschondroplasia (with hemangiomata) → Q78.4
  • Enchondromatosis (cartilaginous) (multiple) → Q78.4
  • Maffucci's syndrome → Q78.4
  • Ollier's disease → Q78.4
  • Bakwin-Krida syndrome (metaphyseal dysplasia) → Q78.5
  • Pyle's syndrome → Q78.5
  • Aclasis, diaphyseal → Q78.6
  • Diaphysial aclasis → Q78.6
  • Caffey's syndrome → Q78.8
  • Leri's pleonosteosis → Q78.8
  • Osteopathia condensans disseminata → Q78.8
  • Osteopoikilosis → Q78.8
  • Stippled epiphyses → Q78.8
  • Synostosis (congenital) → Q78.8
  • Anosteoplasia → Q78.9
  • Chondrodysplasia → Q78.9
  • Chondrodystrophy, chondrodystrophia (familial) (fetalis) (hypoplastic) → Q78.9
  • Osteochondrodysplasia → Q78.9
  • Osteodystrophy → Q78.9
  • Silfversköld's syndrome → Q78.9
  • Brittlebones disease → Q78.0
  • Deafness (acquired) (complete) (hereditary) (partial)with blue sclera and fragility of bone → Q78.0

43 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy