DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

E77 Disorders of glycoprotein metabolism

  • Header · not billable

E77 is not billable. The category heads 4 billable codes in FY2027: the 4 codes directly below it.

Index → code

Where it sits

  1. Chapter 4 Endocrine, nutritional and metabolic diseases (E00-E89)
  2. E70-E88 Metabolic disorders (E70-E88)
  3. E77 Disorders of glycoprotein metabolism
Billable codes
4
Subdivisions
4
CC / MCC codes
0 / 0
HCC V28 codes
0
New FY2027
0
Index entries
20

Codes in E77

  1. E77.0
    Defects in post-translational modification of lysosomal enzymes
    Billable
    Inclusion terms 2

    Inclusion terms

    • Mucolipidosis II [I-cell disease]
    • Mucolipidosis III [pseudo-Hurler polydystrophy]
  2. E77.1
    Defects in glycoprotein degradation
    Billable
    Inclusion terms 4

    Inclusion terms

    • Aspartylglucosaminuria
    • Fucosidosis
    • Mannosidosis
    • Sialidosis [mucolipidosis I]
  3. E77.8
    Other disorders of glycoprotein metabolism
    Billable
  4. E77.9
    Disorder of glycoprotein metabolism, unspecified
    Billable

Sources of each column.

Instructions

Notes that also apply

Block E70-E88 instructions (Excludes1 5, Excludes2 1): printed on the block page.

Chapter 4 instructions (Notes 1, Excludes1 1): printed on the chapter 4 page.

Index entries

  • Polydystrophy, pseudo-Hurler → E77.0
  • Pseudo-Hurler's polydystrophy → E77.0
  • Aspartylglucosaminuria → E77.1
  • Fucosidosis → E77.1
  • Mannosidosis → E77.1
  • Sialidosis → E77.1
  • Hypoproteinemia → E77.8
  • Defect, defectivelysosomal enzyme, post-translational modification → E77.0
  • Defect, defectivemodification, lysosomal enzymes, post-translational → E77.0
  • Disease, diseasedI-cell → E77.0
  • Disease, diseasedpseudo-Hurler's → E77.0
  • MucolipidosisII, III → E77.0
  • Defect, defectivedegradation, glycoprotein → E77.1
  • Defect, defectiveglycoprotein degradation → E77.1
  • MucolipidosisI → E77.1
  • Syndromecarbohydrate-deficient glycoprotein (CDGS) → E77.8
  • Disorder (of)glycoprotein metabolism → E77.9
  • Disorder (of)glycoprotein metabolismspecified NEC → E77.8
  • Disorder (of)metabolism NOSglycoprotein → E77.9
  • Disorder (of)metabolism NOSglycoproteinspecified NEC → E77.8

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy