DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

E78.1 diagnosis code · Billable code · FY2027

E78.1 Pure hyperglyceridemia

  • Billable
  • Not CC/MCC
  • POA reported

E78.1 ICD-10 code: a billable diagnosis code in FY2027, one of 18 billable codes in category E78.

Where it sits

  1. Chapter 4 Endocrine, nutritional and metabolic diseases (E00-E89)
  2. E70-E88 Metabolic disorders (E70-E88)
  3. E78 Disorders of lipoprotein metabolism and other lipidemias
  4. E78.1 Pure hyperglyceridemia
CC / MCC
Neither
MS-DRG
642
HCC V28
–
POA
Reported
Code Editor
–
Index entries
16

Instructions

At E78.1

Inclusion terms

  • Elevated fasting triglycerides
  • Endogenous hyperglyceridemia
  • Fredrickson's hyperlipoproteinemia, type IV
  • Hyperlipidemia, group B
  • Hyperprebetalipoproteinemia
  • Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia

Notes that also apply

Excludes1 from E78

Block E70-E88 instructions (Excludes1 5, Excludes2 1): printed on the block page.

Chapter 4 instructions (Notes 1, Excludes1 1): printed on the chapter 4 page.

Index entries

  • Hyperglyceridemia (endogenous) (essential) (familial) (hereditary) (pure) → E78.1
  • Hyperprebetalipoproteinemia (familial) → E78.1
  • Hypertriglyceridemia, essential → E78.1
  • Prebetalipoproteinemia (acquired) (essential) (familial) (hereditary) (primary) (secondary) → E78.1
  • Very-low-density-lipoprotein-type (VLDL) hyperlipoproteinemia → E78.1
  • Dyslipidemiaelevated fasting triglycerides → E78.1
  • Elevated, elevationfasting triglycerides → E78.1
  • Elevated, elevationtriglycerides → E78.1
  • Frederickson's hyperlipoproteinemia, typeIV → E78.1
  • Hightriglycerides → E78.1
  • Hyperlipoproteinemiavery-low-density-lipoprotein-type (VLDL) → E78.1
  • Lipoproteinemiahyper-pre-beta → E78.1
  • Findings, abnormal, inconclusive, without diagnosistriglycerideshigh → E78.1
  • Hyperlipemia, hyperlipidemiagroupB → E78.1
  • HyperlipoproteinemiaFredrickson's typeIV → E78.1
  • Xanthoma (s), xanthomatosis (primary) (familial) (hereditary)withhyperlipoproteinemiaType IV → E78.1

NCHS Alphabetic Index. Index first, then the Tabular List.

Medicare grouping and edits

CMS files for E78.1
CC / MCCNeither
Appendix BMDC 10 Endocrine, Nutritional and Metabolic Diseases and Disorders, MS-DRG 642 (Inborn and Other Disorders of Metabolism…)
Code Editor–
POAReported
HCC V28–

CMS: MS-DRG v44 (Appendix B, C), MCE v44, POA list FY2027, 2027 Initial ICD-10-CM Mappings. What the rows mean.

Hierarchy