DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

N00 Acute nephritic syndrome

  • Header · not billable

N00 is not billable. The category heads 13 billable codes in FY2027, grouped under 12 subdivisions.

Index → code

  • Glomerulonephritisacute → N00.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)war → N00.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acute → N00.9

Where it sits

  1. Chapter 14 Diseases of the genitourinary system (N00-N99)
  2. N00-N08 Glomerular diseases (N00-N08)
  3. N00 Acute nephritic syndrome
Billable codes
13
Subdivisions
12
CC / MCC codes
0 / 13
HCC V28 codes
0
New FY2027
0
Index entries
21

Codes in N00

  1. N00.0
    Acute nephritic syndrome with minor glomerular abnormality
    BillableMCC
    Inclusion terms 1

    Inclusion terms

    • Acute nephritic syndrome with minimal change lesion
  2. N00.1
    Acute nephritic syndrome with focal and segmental glomerular lesions
    BillableMCC
    Inclusion terms 3

    Inclusion terms

    • Acute nephritic syndrome with focal and segmental hyalinosis
    • Acute nephritic syndrome with focal and segmental sclerosis
    • Acute nephritic syndrome with focal glomerulonephritis
  3. N00.2
    Acute nephritic syndrome with diffuse membranous glomerulonephritis
    BillableMCC
  4. N00.3
    Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
    BillableMCC
  5. N00.4
    Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
    BillableMCC
  6. N00.5
    Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
    BillableMCC
    Excludes1 2

    Excludes1

    • Acute nephritic syndrome with C3 glomerulonephritis (N00.A) N00.A
    • Acute nephritic syndrome with C3 glomerulopathy (N00.A) N00.A
  7. N00.6
    Acute nephritic syndrome with dense deposit disease
    BillableMCC
    Inclusion terms 2

    Inclusion terms

    • Acute nephritic syndrome with C3 glomerulopathy with dense deposit disease
    • Acute nephritic syndrome with membranoproliferative glomerulonephritis, type 2
  8. N00.7
    Acute nephritic syndrome with diffuse crescentic glomerulonephritis
    BillableMCC
    Inclusion terms 1

    Inclusion terms

    • Acute nephritic syndrome with extracapillary glomerulonephritis
  9. N00.8
    Acute nephritic syndrome with other morphologic changes
    BillableMCC
    Inclusion terms 1

    Inclusion terms

    • Acute nephritic syndrome with proliferative glomerulonephritis NOS
  10. N00.9
    Acute nephritic syndrome with unspecified morphologic changes
    BillableMCC
  11. N00.A
    Acute nephritic syndrome with C3 glomerulonephritis
    BillableMCC
    Inclusion terms 1, Excludes1 1

    Inclusion terms

    • Acute nephritic syndrome with C3 glomerulopathy, NOS

    Excludes1

    • Acute nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N00.6) N00.6
  12. N00.B
    Acute nephritic syndrome with immune complex membranoproliferative glomerulonephritis
    Header
  13. N00.B1
    Acute nephritic syndrome with idiopathic immune membranoproliferative glomerulonephritis (IC-MPGN)
    BillableMCC
  14. N00.B2
    Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
    BillableMCC

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At N00

Includes

  • acute glomerular disease
  • acute glomerulonephritis
  • acute nephritis

Excludes1

  • acute tubulo-interstitial nephritis (N10) N10
  • nephritic syndrome NOS (N05.-) N05

Notes that also apply

Block N00-N08 instructions (Excludes1 1, Code also 1): printed on the block page.

Chapter 14 instructions (Excludes2 8): printed on the chapter 14 page.

Index entries

  • Glomerulonephritisacute → N00.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acute → N00.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)croupous → N00.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)war → N00.9
  • Glomerulonephritispoststreptococcal NECacute → N00.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)poststreptococcalacute → N00.9
  • Syndromenephriticacute → N00.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithminor glomerular abnormality → N00.0
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithfocal and segmental glomerular lesions → N00.1
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithdense deposit disease → N00.6
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithspecified morphological changes NEC → N00.8
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithidiopathic immune membranoproliferative glomerulonephritis (IC-MPGN) → N00.B1
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithsecondary immune complex membranoproliferative glomerulonephritis (IC-MPGN) → N00.B2
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithdiffusemembranous glomerulonephritis → N00.2
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithdiffusemesangial proliferative glomerulonephritis → N00.3
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithdiffuseendocapillary proliferative glomerulonephritis → N00.4
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithdiffusemesangiocapillary glomerulonephritis → N00.5
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithdiffusecrescentic glomerulonephritis → N00.7
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithC3glomerulonephritis → N00.A
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithC3glomerulopathy → N00.A
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)acutewithC3glomerulopathywith dense deposit disease → N00.6

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy