DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

N04 Nephrotic syndrome

  • Header · not billable

N04 is not billable. The category heads 16 billable codes in FY2027, grouped under 12 subdivisions.

Index → code

  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital) → N04.9
  • Anasarcarenal → N04.9
  • Lipoidnephrosis → N04.9

Where it sits

  1. Chapter 14 Diseases of the genitourinary system (N00-N99)
  2. N00-N08 Glomerular diseases (N00-N08)
  3. N04 Nephrotic syndrome
Billable codes
16
Subdivisions
12
CC / MCC codes
16 / 0
HCC V28 codes
0
New FY2027
0
Index entries
36

Codes in N04

  1. N04.0
    Nephrotic syndrome with minor glomerular abnormality
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Nephrotic syndrome with minimal change lesion
  2. N04.1
    Nephrotic syndrome with focal and segmental glomerular lesions
    BillableCC
    Inclusion terms 3

    Inclusion terms

    • Nephrotic syndrome with focal and segmental hyalinosis
    • Nephrotic syndrome with focal and segmental sclerosis
    • Nephrotic syndrome with focal glomerulonephritis
  3. N04.2
    Nephrotic syndrome with diffuse membranous glomerulonephritis
    Header
  4. N04.20
    Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Membranous nephropathy NOS with nephrotic syndrome
  5. N04.21
    Primary membranous nephropathy with nephrotic syndrome
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Idiopathic membranous nephropathy with nephrotic syndrome
  6. N04.22
    Secondary membranous nephropathy with nephrotic syndrome
    BillableCC
    Code first 1, Use additional code 1

    Code first

    • , if applicable, other disease or disorder or poisoning causing membranous nephropathy

    Use additional code

    • code, if applicable, for adverse effect of drug causing membranous nephropathy
  7. N04.29
    Other nephrotic syndrome with diffuse membranous glomerulonephritis
    BillableCC
  8. N04.3
    Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
    BillableCC
  9. N04.4
    Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
    BillableCC
  10. N04.5
    Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
    BillableCC
    Excludes1 2

    Excludes1

    • Nephrotic syndrome with C3 glomerulonephritis (N04.A) N04.A
    • Nephrotic syndrome with C3 glomerulopathy (N04.A) N04.A
  11. N04.6
    Nephrotic syndrome with dense deposit disease
    BillableCC
    Inclusion terms 2

    Inclusion terms

    • Nephrotic syndrome with C3 glomerulopathy with dense deposit disease
    • Nephrotic syndrome with membranoproliferative glomerulonephritis, type 2
  12. N04.7
    Nephrotic syndrome with diffuse crescentic glomerulonephritis
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Nephrotic syndrome with extracapillary glomerulonephritis
  13. N04.8
    Nephrotic syndrome with other morphologic changes
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Nephrotic syndrome with proliferative glomerulonephritis NOS
  14. N04.9
    Nephrotic syndrome with unspecified morphologic changes
    BillableCC
  15. N04.A
    Nephrotic syndrome with C3 glomerulonephritis
    BillableCC
    Inclusion terms 1, Excludes1 1

    Inclusion terms

    • Nephrotic syndrome with C3 glomerulopathy

    Excludes1

    • Nephrotic syndrome (with C3 glomerulopathy) with dense deposit disease (N04.6) N04.6
  16. N04.B
    Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
    Header
  17. N04.B1
    Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)
    BillableCC
  18. N04.B2
    Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
    BillableCC

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At N04

Includes

  • congenital nephrotic syndrome
  • lipoid nephrosis

Notes that also apply

Block N00-N08 instructions (Excludes1 1, Code also 1): printed on the block page.

Chapter 14 instructions (Excludes2 8): printed on the chapter 14 page.

Index entries

  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital) → N04.9
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital)minimal change → N04.0
  • Anasarcarenal → N04.9
  • Disease, diseasedfoot process → N04.9
  • Lipoidnephrosis → N04.9
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital)acute → N04.9
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital)lipoid → N04.9
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital)radiation → N04.9
  • Syndromenephrotic (congenital) → N04.9
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital)withglomerular lesion → N04.1
  • Nephropathymembranous (diffuse)idiopathic, with nephrotic syndrome → N04.21
  • Syndromenephrotic (congenital)specified type NEC with diffuse membranous glomerulonephritis → N04.29
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital)withhypocomplementemic → N04.5
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)withfoot process disease → N04.9
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital)withfoot process disease → N04.9
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital)tubular (acute)radiation → N04.9
  • Syndromeidiopathicnephrotic (infantile) → N04.9
  • Syndromenephrotic (congenital)withminor glomerular abnormality → N04.0
  • Syndromenephrotic (congenital)withfocal and segmental glomerular lesions → N04.1
  • Nephropathymembranous (diffuse)withnephrotic syndrome → N04.20
  • Nephropathymembranous (diffuse)primarywith nephrotic syndrome → N04.21
  • Nephropathymembranous (diffuse)secondarywith nephrotic syndrome → N04.22
  • Syndromenephrotic (congenital)withdense deposit disease → N04.6
  • Syndromenephrotic (congenital)withspecified morphological changes NEC → N04.8
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)withglomerular lesionidiopathic immune membranoproliferative glomerulonephritis (IC-MPGN) → N04.B1
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)withglomerular lesionsecondary immune complex membranoproliferative glomerulonephritis (IC-MPGN) → N04.B2
  • Syndromenephrotic (congenital)withdiffusemembranous glomerulonephritis → N04.20
  • Nephropathymembranous (diffuse)withnephrotic syndromeprimary → N04.21
  • Nephropathymembranous (diffuse)withnephrotic syndromesecondary → N04.22
  • Syndromenephrotic (congenital)withdiffusemesangial proliferative glomerulonephritis → N04.3
  • Syndromenephrotic (congenital)withdiffuseendocapillary proliferative glomerulonephritis → N04.4
  • Syndromenephrotic (congenital)withdiffusemesangiocapillary glomerulonephritis → N04.5
  • Syndromenephrotic (congenital)withdiffusecrescentic glomerulonephritis → N04.7
  • Syndromenephrotic (congenital)withC3glomerulonephritis → N04.A
  • Syndromenephrotic (congenital)withC3glomerulopathy → N04.A
  • Syndromenephrotic (congenital)withC3glomerulopathywith dense deposit disease → N04.6

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy