DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

N01 Rapidly progressive nephritic syndrome

  • Header · not billable

N01 is not billable. The category heads 11 billable codes in FY2027: the 11 codes directly below it.

Index → code

  • Glomerulonephritissubacute → N01.9
  • Glomerulonephritisrapidly progressive → N01.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)subacute → N01.9

Where it sits

  1. Chapter 14 Diseases of the genitourinary system (N00-N99)
  2. N00-N08 Glomerular diseases (N00-N08)
  3. N01 Rapidly progressive nephritic syndrome
Billable codes
11
Subdivisions
11
CC / MCC codes
0 / 11
HCC V28 codes
0
New FY2027
0
Index entries
22

Codes in N01

  1. N01.0
    Rapidly progressive nephritic syndrome with minor glomerular abnormality
    BillableMCC
    Inclusion terms 1

    Inclusion terms

    • Rapidly progressive nephritic syndrome with minimal change lesion
  2. N01.1
    Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
    BillableMCC
    Inclusion terms 3

    Inclusion terms

    • Rapidly progressive nephritic syndrome with focal and segmental hyalinosis
    • Rapidly progressive nephritic syndrome with focal and segmental sclerosis
    • Rapidly progressive nephritic syndrome with focal glomerulonephritis
  3. N01.2
    Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
    BillableMCC
  4. N01.3
    Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
    BillableMCC
  5. N01.4
    Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
    BillableMCC
  6. N01.5
    Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
    BillableMCC
    Inclusion terms 1, Excludes1 2

    Inclusion terms

    • Rapidly progressive nephritic syndrome with membranoproliferative glomerulonephritis, types 1 and 3, or NOS

    Excludes1

    • Rapidly progressive nephritic syndrome with C3 glomerulonephritis (N01.A) N01.A
    • Rapidly progressive nephritic syndrome with C3 glomerulopathy (N01.A) N01.A
  7. N01.6
    Rapidly progressive nephritic syndrome with dense deposit disease
    BillableMCC
    Inclusion terms 2

    Inclusion terms

    • Rapidly progressive nephritic syndrome with C3 glomerulopathy with dense deposit disease
    • Rapidly progressive nephritic syndrome with membranoproliferative glomerulonephritis, type 2
  8. N01.7
    Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
    BillableMCC
    Inclusion terms 1

    Inclusion terms

    • Rapidly progressive nephritic syndrome with extracapillary glomerulonephritis
  9. N01.8
    Rapidly progressive nephritic syndrome with other morphologic changes
    BillableMCC
    Inclusion terms 1

    Inclusion terms

    • Rapidly progressive nephritic syndrome with proliferative glomerulonephritis NOS
  10. N01.9
    Rapidly progressive nephritic syndrome with unspecified morphologic changes
    BillableMCC
  11. N01.A
    Rapidly progressive nephritic syndrome with C3 glomerulonephritis
    BillableMCC
    Inclusion terms 1, Excludes1 1

    Inclusion terms

    • Rapidly progressive nephritic syndrome with C3 glomerulopathy, NOS

    Excludes1

    • Rapidly progressive nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N01.6) N01.6

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At N01

Includes

  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Excludes1

  • nephritic syndrome NOS (N05.-) N05

Notes that also apply

Block N00-N08 instructions (Excludes1 1, Code also 1): printed on the block page.

Chapter 14 instructions (Excludes2 8): printed on the chapter 14 page.

Index entries

  • Glomerulonephritisrapidly progressive → N01.9
  • Glomerulonephritissubacute → N01.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressive → N01.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)subacute → N01.9
  • Disease, diseasedglomerularrapidly progressive → N01.9
  • Disease, diseasedrenal (functional) (pelvis)rapidly progressive → N01.9
  • Disease, diseasedrenal (functional) (pelvis)subacute → N01.9
  • Glomerulonephritispoststreptococcal NECrapidly progressive → N01.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)poststreptococcalrapidly progressive → N01.9
  • Syndromenephriticrapidly progressive → N01.9
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithminor glomerular abnormality → N01.0
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithfocal and segmental glomerular lesions → N01.1
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithdense deposit disease → N01.6
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithspecified morphological changes NEC → N01.8
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithdiffusemembranous glomerulonephritis → N01.2
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithdiffusemesangial proliferative glomerulonephritis → N01.3
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithdiffuseendocapillary proliferative glomerulonephritis → N01.4
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithdiffusemesangiocapillary glomerulonephritis → N01.5
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithdiffusecrescentic glomerulonephritis → N01.7
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithC3glomerulonephritis → N01.A
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithC3glomerulopathy → N01.A
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)rapidly progressivewithC3glomerulopathywith dense deposit disease → N01.6

NCHS Alphabetic Index. Index first, then the Tabular List.

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