DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q41 Congenital absence, atresia and stenosis of small intestine

  • Header · not billable

Q41 is not billable. The category heads 5 billable codes in FY2027: the 5 codes directly below it.

Index → code

  • Apple peel syndrome → Q41.1
  • Agenesisileum → Q41.2
  • Agenesisjejunum → Q41.1

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q38-Q45 Other congenital malformations of the digestive system (Q38-Q45)
  3. Q41 Congenital absence, atresia and stenosis of small intestine
Billable codes
5
Subdivisions
5
CC / MCC codes
5 / 0
HCC V28 codes
5
New FY2027
0
Index entries
29

Codes in Q41

  1. Q41.0
    Congenital absence, atresia and stenosis of duodenum
    BillableCC78Exempt
  2. Q41.1
    Congenital absence, atresia and stenosis of jejunum
    BillableCC78Exempt
    Inclusion terms 2

    Inclusion terms

    • Apple peel syndrome
    • Imperforate jejunum
  3. Q41.2
    Congenital absence, atresia and stenosis of ileum
    BillableCC78Exempt
  4. Q41.8
    Congenital absence, atresia and stenosis of other specified parts of small intestine
    BillableCC78Exempt
  5. Q41.9
    Congenital absence, atresia and stenosis of small intestine, part unspecified
    BillableCC78Exempt
    Inclusion terms 1

    Inclusion terms

    • Congenital absence, atresia and stenosis of intestine NOS

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At Q41

Includes

  • congenital obstruction, occlusion or stricture of small intestine or intestine NOS

Excludes1

  • cystic fibrosis with intestinal manifestation (E84.11) E84.11
  • meconium ileus NOS (without cystic fibrosis) (P76.0) P76.0

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Apple peel syndrome → Q41.1
  • Agenesisduodenum → Q41.0
  • Atresia, atreticduodenum → Q41.0
  • Agenesisjejunum → Q41.1
  • Anomaly, anomalous (congenital) (unspecified type)apple peel syndrome → Q41.1
  • Atresia, atreticjejunum → Q41.1
  • Imperforate (congenital)jejunum → Q41.1
  • Agenesisileum → Q41.2
  • Atresia, atreticileum → Q41.2
  • Agenesisintestine (small) → Q41.9
  • Atresia, atreticintestine (small) → Q41.9
  • Hypoplasia, hypoplasticintestine (small) → Q41.9
  • Impervious (congenital)intestine (small) → Q41.9
  • Absence (of) (organ or part) (complete or partial)duodenum (acquired)congenital → Q41.0
  • Stenosis, stenotic (cicatricial)duodenumcongenital → Q41.0
  • Strictureduodenumcongenital → Q41.0
  • Absence (of) (organ or part) (complete or partial)jejunum (acquired)congenital → Q41.1
  • Stenosis, stenotic (cicatricial)jejunumcongenital → Q41.1
  • Stricturejejunumcongenital → Q41.1
  • Absence (of) (organ or part) (complete or partial)ileum (acquired)congenital → Q41.2
  • Stenosis, stenotic (cicatricial)ileumcongenital → Q41.2
  • Strictureileumcongenital → Q41.2
  • Absence (of) (organ or part) (complete or partial)intestine (acquired) (small)congenital → Q41.9
  • Obstruction, obstructed, obstructiveintestinecongenital (small) → Q41.9
  • Stenosis, stenotic (cicatricial)intestinecongenital (small) → Q41.9
  • Strictureintestinecongenital (small) → Q41.9
  • Absence (of) (organ or part) (complete or partial)intestine (acquired) (small)congenitalspecified NEC → Q41.8
  • Stenosis, stenotic (cicatricial)intestinecongenital (small)specified NEC → Q41.8
  • Strictureintestinecongenital (small)specified NEC → Q41.8

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy