DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q42 Congenital absence, atresia and stenosis of large intestine

  • Header · not billable

Q42 is not billable. The category heads 6 billable codes in FY2027: the 6 codes directly below it.

Index → code

  • Agenesiscecum → Q42.8
  • Agenesiscolon → Q42.9
  • Agenesisrectum → Q42.1

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q38-Q45 Other congenital malformations of the digestive system (Q38-Q45)
  3. Q42 Congenital absence, atresia and stenosis of large intestine
Billable codes
6
Subdivisions
6
CC / MCC codes
6 / 0
HCC V28 codes
6
New FY2027
0
Index entries
71

Codes in Q42

  1. Q42.0
    Congenital absence, atresia and stenosis of rectum with fistula
    BillableCC78Exempt
  2. Q42.1
    Congenital absence, atresia and stenosis of rectum without fistula
    BillableCC78Exempt
    Inclusion terms 1

    Inclusion terms

    • Imperforate rectum
  3. Q42.2
    Congenital absence, atresia and stenosis of anus with fistula
    BillableCC78Exempt
  4. Q42.3
    Congenital absence, atresia and stenosis of anus without fistula
    BillableCC78Exempt
    Inclusion terms 1

    Inclusion terms

    • Imperforate anus
  5. Q42.8
    Congenital absence, atresia and stenosis of other parts of large intestine
    BillableCC78Exempt
  6. Q42.9
    Congenital absence, atresia and stenosis of large intestine, part unspecified
    BillableCC78Exempt

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At Q42

Includes

  • congenital obstruction, occlusion and stricture of large intestine

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Absence (of) (organ or part) (complete or partial)rectum (congenital) → Q42.1
  • Agenesisrectum → Q42.1
  • Atresia, atreticrectum → Q42.1
  • Hypoplasia, hypoplasticrectum → Q42.1
  • Imperforate (congenital)rectum → Q42.1
  • Impervious (congenital)rectum → Q42.1
  • Absence (of) (organ or part) (complete or partial)anus (congenital) → Q42.3
  • Agenesisanus, anal (canal) → Q42.3
  • Atresia, atreticani, anus, anal (canal) → Q42.3
  • Hypoplasia, hypoplasticanus, anal (canal) → Q42.3
  • Imperforate (congenital)anus → Q42.3
  • Impervious (congenital)anus → Q42.3
  • Persistence, persistent (congenital)anal membrane → Q42.3
  • Septum, septate (congenital)anal → Q42.3
  • Absence (of) (organ or part) (complete or partial)appendix, congenital → Q42.8
  • Agenesisappendix → Q42.8
  • Agenesiscecum → Q42.8
  • Atresia, atreticcecum → Q42.8
  • Hypoplasia, hypoplasticcecum → Q42.8
  • Agenesiscolon → Q42.9
  • Atresia, atreticcolon → Q42.9
  • Hypoplasia, hypoplasticcolon → Q42.9
  • Absence (of) (organ or part) (complete or partial)rectum (congenital)with fistula → Q42.0
  • Agenesisrectumwith fistula → Q42.0
  • Atresia, atreticrectumwith fistula → Q42.0
  • Hypoplasia, hypoplasticrectumwith fistula → Q42.0
  • Imperforate (congenital)rectumwith fistula → Q42.0
  • Impervious (congenital)rectumwith fistula → Q42.0
  • Stricturerectum (sphincter)congenital → Q42.1
  • Absence (of) (organ or part) (complete or partial)anus (congenital)with fistula → Q42.2
  • Agenesisanus, anal (canal)with fistula → Q42.2
  • Atresia, atreticani, anus, anal (canal)with fistula → Q42.2
  • Hypoplasia, hypoplasticanus, anal (canal)with fistula → Q42.2
  • Imperforate (congenital)anuswith fistula → Q42.2
  • Impervious (congenital)anuswith fistula → Q42.2
  • Persistence, persistent (congenital)anal membranewith fistula → Q42.2
  • Septum, septate (congenital)analwith fistula → Q42.2
  • Occlusion, occludedanuscongenital → Q42.3
  • Stenosis, stenotic (cicatricial)anus, anal (canal) (sphincter)congenital → Q42.3
  • Strictureanus (sphincter)congenital → Q42.3

31 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy