DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q44 Congenital malformations of gallbladder, bile ducts and liver

  • Header · not billable

Q44 is not billable. The category heads 10 billable codes in FY2027, grouped under 8 subdivisions.

Index → code

  • Intrahepatic gallbladder → Q44.1
  • Alagille (-Watson) syndrome → Q44.71
  • Agenesisliver → Q44.79

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q38-Q45 Other congenital malformations of the digestive system (Q38-Q45)
  3. Q44 Congenital malformations of gallbladder, bile ducts and liver
Billable codes
10
Subdivisions
8
CC / MCC codes
8 / 2
HCC V28 codes
3
New FY2027
0
Index entries
93

Codes in Q44

  1. Q44.0
    Agenesis, aplasia and hypoplasia of gallbladder
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Congenital absence of gallbladder
  2. Q44.1
    Other congenital malformations of gallbladder
    BillableCCExempt
    Inclusion terms 2

    Inclusion terms

    • Congenital malformation of gallbladder NOS
    • Intrahepatic gallbladder
  3. Q44.2
    Atresia of bile ducts
    BillableMCC68Exempt
  4. Q44.3
    Congenital stenosis and stricture of bile ducts
    BillableMCC68Exempt
  5. Q44.4
    Choledochal cyst
    BillableCCExempt
  6. Q44.5
    Other congenital malformations of bile ducts
    BillableCCExempt
    Inclusion terms 4

    Inclusion terms

    • Accessory hepatic duct
    • Biliary duct duplication
    • Congenital malformation of bile duct NOS
    • Cystic duct duplication
  7. Q44.6
    Cystic disease of liver
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Fibrocystic disease of liver
  8. Q44.7
    Other congenital malformations of liver
    Header
    Code also 1

    Code also

    • , if applicable, associated malformations affecting other systems
  9. Q44.70
    Other congenital malformation of liver, unspecified
    BillableCCExempt
    Inclusion terms 1

    Inclusion terms

    • Congenital malformation of liver, NOS
  10. Q44.71
    Alagille syndrome
    BillableCC68Exempt
    Inclusion terms 1

    Inclusion terms

    • Alagille-Watson syndrome
  11. Q44.79
    Other congenital malformations of liver
    BillableCCExempt
    Inclusion terms 3

    Inclusion terms

    • Accessory liver
    • Congenital absence of liver
    • Congenital hepatomegaly

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Intrahepatic gallbladder → Q44.1
  • Alagille (-Watson) syndrome → Q44.71
  • Agenesisgallbladder → Q44.0
  • Aplasiagallbladder, congenital → Q44.0
  • Hypoplasia, hypoplasticgallbladder → Q44.0
  • Accessory (congenital)gallbladder → Q44.1
  • Anomaly, anomalous (congenital) (unspecified type)gallbladder (position) (shape) (size) → Q44.1
  • Atresia, atreticgallbladder → Q44.1
  • Band(s)gallbladder (congenital) → Q44.1
  • Bifurcation (congenital)gallbladder → Q44.1
  • Deformitygallbladder (congenital) → Q44.1
  • Displacement, displacedgallbladder (congenital) → Q44.1
  • Floatinggallbladder, congenital → Q44.1
  • Inclusiongallbladder in liver (congenital) → Q44.1
  • Mobile, mobilitygallbladder, congenital → Q44.1
  • Wanderinggallbladder, congenital → Q44.1
  • Atresia, atreticbile duct (common) (congenital) (hepatic) → Q44.2
  • Atresia, atreticcommon duct → Q44.2
  • Atresia, atreticcystic duct → Q44.2
  • Impervious (congenital)bile duct → Q44.2
  • Cyst (colloid) (mucous) (simple) (retention)choledochus, congenital → Q44.4
  • Aberrant (congenital)hepatic duct → Q44.5
  • Absence (of) (organ or part) (complete or partial)bile, biliary duct, congenital → Q44.5
  • Accessory (congenital)biliary duct or passage → Q44.5
  • Accessory (congenital)cystic duct → Q44.5
  • Accessory (congenital)hepatic ducts → Q44.5
  • Agenesisbile duct or passage → Q44.5
  • Anomaly, anomalous (congenital) (unspecified type)biliary duct or passage → Q44.5
  • Anomaly, anomalous (congenital) (unspecified type)common duct → Q44.5
  • Anomaly, anomalous (congenital) (unspecified type)cystic duct → Q44.5
  • Anomaly, anomalous (congenital) (unspecified type)hepatic duct → Q44.5
  • Deformitybile duct (common) (congenital) (hepatic) → Q44.5
  • Deformitybiliary duct or passage (congenital) → Q44.5
  • Deformitycystic duct (congenital) → Q44.5
  • Deformityhepatic duct (congenital) → Q44.5
  • Distortion(s) (congenital)bile duct or passage → Q44.5
  • Distortion(s) (congenital)common duct → Q44.5
  • Distortion(s) (congenital)cystic duct → Q44.5
  • Distortion(s) (congenital)hepatic duct → Q44.5
  • Duplication, duplexbiliary duct (any) → Q44.5

53 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy