DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

D82 Immunodeficiency associated with other major defects

  • Header · not billable

D82 is not billable. The category heads 7 billable codes in FY2027: the 7 codes directly below it.

Index → code

  • Di George's syndrome → D82.1
  • Alymphoplasia, thymic → D82.1
  • Wiskott-Aldrich syndrome → D82.0

Where it sits

  1. Chapter 3 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
  2. D80-D89 Certain disorders involving the immune mechanism (D80-D89)
  3. D82 Immunodeficiency associated with other major defects
Billable codes
7
Subdivisions
7
CC / MCC codes
2 / 0
HCC V28 codes
2
New FY2027
0
Index entries
29

Codes in D82

  1. D82.0
    Wiskott-Aldrich syndrome
    BillableCC115
    Inclusion terms 1

    Inclusion terms

    • Immunodeficiency with thrombocytopenia and eczema
  2. D82.1
    Di George's syndrome
    BillableCC115
    Inclusion terms 3

    Inclusion terms

    • Pharyngeal pouch syndrome
    • Thymic alymphoplasia
    • Thymic aplasia or hypoplasia with immunodeficiency
  3. D82.2
    Immunodeficiency with short-limbed stature
    Billable
  4. D82.3
    Immunodeficiency following hereditary defective response to Epstein-Barr virus
    Billable
    Inclusion terms 1

    Inclusion terms

    • X-linked lymphoproliferative disease
  5. D82.4
    Hyperimmunoglobulin E [IgE] syndrome
    Billable
  6. D82.8
    Immunodeficiency associated with other specified major defects
    Billable
  7. D82.9
    Immunodeficiency associated with major defect, unspecified
    Billable

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At D82

Excludes1

  • ataxia telangiectasia [Louis-Bar] (G11.3) G11.3

Notes that also apply

Block D80-D89 instructions (Includes 3, Excludes1 2, Excludes2 1): printed on the block page.

Chapter 3 instructions (Excludes2 9): printed on the chapter 3 page.

Index entries

  • Aldrich (-Wiskott) syndrome (eczema-thrombocytopenia) → D82.0
  • Wiskott-Aldrich syndrome → D82.0
  • Alymphoplasia, thymic → D82.1
  • Di George's syndrome → D82.1
  • DiGeorge's syndrome (thymic hypoplasia) → D82.1
  • Pharyngeal pouch syndrome → D82.1
  • Lymphoproliferation, X-linked disease → D82.3
  • SyndromeAldrich (-Wiskott) → D82.0
  • Syndromeeczema-thrombocytopenia → D82.0
  • Syndromefamilial eczema-thrombocytopenia (Wiskott-Aldrich) → D82.0
  • SyndromeWiskott-Aldrich → D82.0
  • Alymphocytosisthymic (with immunodeficiency) → D82.1
  • Aplasiaparathyroid-thymic → D82.1
  • Aplasiathymic, with immunodeficiency → D82.1
  • Dysplasiathymic, with immunodeficiency → D82.1
  • Hypoplasia, hypoplasticthymic, with immunodeficiency → D82.1
  • Syndromedi George's → D82.1
  • Syndromepharyngeal pouch → D82.1
  • Short, shortening, shortnesslimbed stature, with immunodeficiency → D82.2
  • Immunodeficiencyfollowing hereditary defective response to Epstein-Barr virus (EBV) → D82.3
  • Syndromehyperimmunoglobulin E (IgE) → D82.4
  • Immunodeficiencywiththrombocytopenia and eczema → D82.0
  • Hypoplasia, hypoplasticthymus (gland)with immunodeficiency → D82.1
  • Immunodeficiencywithshort-limbed stature → D82.2
  • Disease, diseasedlymphoproliferativeX-linked → D82.3
  • Immunodeficiencywithpartial albinism → D82.8
  • Immunodeficiencywithmajor defect → D82.9
  • Deficiency, deficientimmunitycell-mediatedwith thrombocytopenia and eczema → D82.0
  • Immunodeficiencywithmajor defectspecified type NEC → D82.8

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy