DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Block · Chapter 17

Q00-Q07 Congenital malformations of the nervous system (Q00-Q07)

Block Q00-Q07 groups 8 categories with 45 billable codes in FY2027.

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q00-Q07 Congenital malformations of the nervous system (Q00-Q07)

Neighbouring blocks

Categories
8
Billable codes
45
CC codes
16
MCC codes
7
HCC V28 codes
45
New FY2027
0

Categories in Q00-Q07

  • Q00

    Anencephaly and similar malformations

    Acrania → Q00.0

    • 3 billable codes
    • 3 MCC
    • 3 with HCC
  • Q01

    Encephalocele

    Encephalocele → Q01.9

    • 5 billable codes
    • 5 CC
    • 5 with HCC
  • Q02

    Microcephaly

    Microencephalon → Q02

    • Billable, no subdivisions
    • 1 with HCC
  • Q03

    Congenital hydrocephalus

    Dandy-Walker syndrome → Q03.1

    • 4 billable codes
    • 4 with HCC
  • Q04

    Other congenital malformations of brain

    Agyria → Q04.3

    • 9 billable codes
    • 4 CC
    • 4 MCC
    • 9 with HCC
  • Q05

    Spina bifida

    Spina bifida (aperta) → Q05.9

    • 10 billable codes
    • 5 CC
    • 10 with HCC
  • Q06

    Other congenital malformations of spinal cord

    Amyelia → Q06.0

    • 7 billable codes
    • 7 with HCC
  • Q07

    Other congenital malformations of nervous system

    Gunn's syndrome → Q07.8

    • 6 billable codes
    • 2 CC
    • 6 with HCC

Index main terms

  • Anomaly, anomalous (congenital) (unspecified type) → Q00, Q02, Q03, Q04, Q05, Q06, Q07 (33 entries)
  • Malformation (congenital) → Q04, Q06, Q07 (16 entries)
  • Spina bifida (aperta) → Q05 (16 entries)
  • Deformity → Q00, Q02, Q03, Q04, Q06, Q07 (15 entries)
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent) → Q03, Q05 (13 entries)
  • Agenesis → Q00, Q02, Q03, Q04, Q06, Q07 (12 entries)
  • Hypoplasia, hypoplastic → Q00, Q02, Q03, Q04, Q06 (10 entries)
  • Cyst (colloid) (mucous) (simple) (retention) → Q03, Q04, Q06 (8 entries)
  • Absence (of) (organ or part) (complete or partial) → Q00, Q02, Q03, Q04 (7 entries)
  • Distortion(s) (congenital) → Q00, Q02, Q03, Q04, Q06, Q07 (7 entries)
  • Arnold-Chiari disease, obstruction or syndrome (type II) → Q04, Q07 (6 entries)
  • Aplasia → Q00, Q04, Q06 (5 entries)
  • Encephalocele → Q01 (5 entries)
  • Malposition → Q04, Q06, Q07 (5 entries)
  • Atresia, atretic → Q03 (3 entries)

+74 more main terms; the search box finds them by word.

Block instructions

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.