DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q00 Anencephaly and similar malformations

  • Header · not billable

Q00 is not billable. The category heads 3 billable codes in FY2027: the 3 codes directly below it.

Index → code

  • Acrania → Q00.0
  • Hemianencephaly → Q00.0
  • Anencephalus, anencephaly → Q00.0

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q00-Q07 Congenital malformations of the nervous system (Q00-Q07)
  3. Q00 Anencephaly and similar malformations
Billable codes
3
Subdivisions
3
CC / MCC codes
0 / 3
HCC V28 codes
3
New FY2027
0
Index entries
24

Codes in Q00

  1. Q00.0
    Anencephaly
    BillableMCC182Exempt
    Inclusion terms 5

    Inclusion terms

    • Acephaly
    • Acrania
    • Amyelencephaly
    • Hemianencephaly
    • Hemicephaly
  2. Q00.1
    Craniorachischisis
    BillableMCC182Exempt
  3. Q00.2
    Iniencephaly
    BillableMCC182Exempt

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Acephalia, acephalism, acephalus, acephaly → Q00.0
  • Acrania → Q00.0
  • Amyelencephalus, amyelencephaly → Q00.0
  • Anencephalus, anencephaly → Q00.0
  • Hemianencephaly → Q00.0
  • Hemicephalus, hemicephaly → Q00.0
  • Craniorachischisis (totalis) → Q00.1
  • Iniencephalus, iniencephaly → Q00.2
  • Absence (of) (organ or part) (complete or partial)brain → Q00.0
  • Agenesisbrain → Q00.0
  • Anomaly, anomalous (congenital) (unspecified type)hemianencephaly → Q00.0
  • Anomaly, anomalous (congenital) (unspecified type)hemicephaly → Q00.0
  • Anomaly, anomalous (congenital) (unspecified type)hemicrania → Q00.0
  • Aplasiabrain → Q00.0
  • Hemicraniacongenital malformation → Q00.0
  • Monster, monstrosity (single)acephalic → Q00.0
  • Absence (of) (organ or part) (complete or partial)skull bone (congenital)withanencephaly → Q00.0
  • Agenesisskull (bone)withanencephaly → Q00.0
  • Anomaly, anomalous (congenital) (unspecified type)skullwithanencephaly → Q00.0
  • Distortion(s) (congenital)skull bone(s) NECwithanencephalus → Q00.0
  • Hypoplasia, hypoplasticskull (bone)withanencephaly → Q00.0
  • Anomaly, anomalous (congenital) (unspecified type)boneskullwithanencephaly → Q00.0
  • Deformityskull (acquired)congenitalwithanencephaly → Q00.0
  • Imperfectclosure (congenital)skullwithanencephaly → Q00.0

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy