DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q05 Spina bifida

  • Header · not billable

Q05 is not billable. The category heads 10 billable codes in FY2027: the 10 codes directly below it.

Index → code

  • Spina bifida (aperta) → Q05.9
  • Spina bifida (aperta)dorsal → Q05.6
  • Spina bifida (aperta)lumbar → Q05.7
Billable codes
10
Subdivisions
10
CC / MCC codes
5 / 0
HCC V28 codes
10
New FY2027
0
Index entries
25

Codes in Q05

  1. Q05.0
    Cervical spina bifida with hydrocephalus
    BillableCC182Exempt
  2. Q05.1
    Thoracic spina bifida with hydrocephalus
    BillableCC182Exempt
    Inclusion terms 2

    Inclusion terms

    • Dorsal spina bifida with hydrocephalus
    • Thoracolumbar spina bifida with hydrocephalus
  3. Q05.2
    Lumbar spina bifida with hydrocephalus
    BillableCC182Exempt
    Inclusion terms 1

    Inclusion terms

    • Lumbosacral spina bifida with hydrocephalus
  4. Q05.3
    Sacral spina bifida with hydrocephalus
    BillableCC182Exempt
  5. Q05.4
    Unspecified spina bifida with hydrocephalus
    BillableCC182Exempt
  6. Q05.5
    Cervical spina bifida without hydrocephalus
    Billable182Exempt
  7. Q05.6
    Thoracic spina bifida without hydrocephalus
    Billable182Exempt
    Inclusion terms 2

    Inclusion terms

    • Dorsal spina bifida NOS
    • Thoracolumbar spina bifida NOS
  8. Q05.7
    Lumbar spina bifida without hydrocephalus
    Billable182Exempt
    Inclusion terms 1

    Inclusion terms

    • Lumbosacral spina bifida NOS
  9. Q05.8
    Sacral spina bifida without hydrocephalus
    Billable182Exempt
  10. Q05.9
    Spina bifida, unspecified
    Billable182Exempt

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At Q05

Includes

  • hydromeningocele (spinal)
  • meningocele (spinal)
  • meningomyelocele
  • myelocele
  • myelomeningocele
  • rachischisis
  • spina bifida (aperta)(cystica)
  • syringomyelocele

Excludes1

  • Arnold-Chiari syndrome, type II (Q07.0-) Q07.0
  • spina bifida occulta (Q76.0) Q76.0

Use additional code

  • code for any associated paraplegia (paraparesis) (G82.2-) G82.2

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Spina bifida (aperta) → Q05.9
  • Spina bifida (aperta)with hydrocephalus NEC → Q05.4
  • Spina bifida (aperta)cervical → Q05.5
  • Spina bifida (aperta)dorsal → Q05.6
  • Spina bifida (aperta)thoracic → Q05.6
  • Spina bifida (aperta)thoracolumbar → Q05.6
  • Spina bifida (aperta)lumbar → Q05.7
  • Spina bifida (aperta)lumbosacral → Q05.7
  • Spina bifida (aperta)sacral → Q05.8
  • Anomaly, anomalous (congenital) (unspecified type)meningocele → Q05.9
  • Spina bifida (aperta)cervicalwith hydrocephalus → Q05.0
  • Spina bifida (aperta)dorsalwith hydrocephalus → Q05.1
  • Spina bifida (aperta)thoracicwith hydrocephalus → Q05.1
  • Spina bifida (aperta)thoracolumbarwith hydrocephalus → Q05.1
  • Spina bifida (aperta)lumbarwith hydrocephalus → Q05.2
  • Spina bifida (aperta)lumbosacralwith hydrocephalus → Q05.2
  • Spina bifida (aperta)sacralwith hydrocephalus → Q05.3
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)with spina bifida → Q05.4
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)with spina bifidacervical → Q05.0
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)with spina bifidadorsal → Q05.1
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)with spina bifidathoracic → Q05.1
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)with spina bifidathoracolumbar → Q05.1
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)with spina bifidalumbar → Q05.2
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)with spina bifidalumbosacral → Q05.2
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)with spina bifidasacral → Q05.3

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy