DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q07 Other congenital malformations of nervous system

  • Header · not billable

Q07 is not billable. The category heads 6 billable codes in FY2027, grouped under 3 subdivisions.

Index → code

  • Gunn's syndrome → Q07.8
  • Marcus Gunn's syndrome → Q07.8
  • Jaw-winking phenomenon or syndrome → Q07.8

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q00-Q07 Congenital malformations of the nervous system (Q00-Q07)
  3. Q07 Other congenital malformations of nervous system
Billable codes
6
Subdivisions
3
CC / MCC codes
2 / 0
HCC V28 codes
6
New FY2027
0
Index entries
51

Codes in Q07

  1. Q07.0
    Arnold-Chiari syndrome
    Header
    Inclusion terms 1, Excludes1 2

    Inclusion terms

    • Arnold-Chiari syndrome, type II

    Excludes1

    • Arnold-Chiari syndrome, type III (Q01.-) Q01
    • Arnold-Chiari syndrome, type IV (Q04.8) Q04.8
  2. Q07.00
    Arnold-Chiari syndrome without spina bifida or hydrocephalus
    Billable182Exempt
  3. Q07.01
    Arnold-Chiari syndrome with spina bifida
    Billable182Exempt
  4. Q07.02
    Arnold-Chiari syndrome with hydrocephalus
    BillableCC182Exempt
  5. Q07.03
    Arnold-Chiari syndrome with spina bifida and hydrocephalus
    BillableCC182Exempt
  6. Q07.8
    Other specified congenital malformations of nervous system
    Billable182Exempt
    Inclusion terms 4

    Inclusion terms

    • Agenesis of nerve
    • Displacement of brachial plexus
    • Jaw-winking syndrome
    • Marcus Gunn's syndrome
  7. Q07.9
    Congenital malformation of nervous system, unspecified
    Billable182Exempt
    Inclusion terms 3

    Inclusion terms

    • Congenital anomaly NOS of nervous system
    • Congenital deformity NOS of nervous system
    • Congenital disease or lesion NOS of nervous system

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At Q07

Excludes2

  • congenital central alveolar hypoventilation syndrome (G47.35) G47.35
  • familial dysautonomia [Riley-Day] (G90.1) G90.1
  • neurofibromatosis (nonmalignant) (Q85.0-) Q85.0

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Arnold-Chiari disease, obstruction or syndrome (type II) → Q07.00
  • Gunn's syndrome → Q07.8
  • Jaw-winking phenomenon or syndrome → Q07.8
  • Marcus Gunn's syndrome → Q07.8
  • Accessory (congenital)nervous system, part NEC → Q07.8
  • Agenesisnerve → Q07.8
  • Agenesisnervous system, part NEC → Q07.8
  • Agenesisnuclear → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)acoustic nerve → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)sense organs NEC → Q07.8
  • Displacement, displacedbrachial plexus (congenital) → Q07.8
  • Distortion(s) (congenital)nerve → Q07.8
  • Phenomenonjaw-winking → Q07.8
  • Syndromejaw-winking → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)gyri → Q07.9
  • Anomaly, anomalous (congenital) (unspecified type)meningeal bands or folds → Q07.9
  • Anomaly, anomalous (congenital) (unspecified type)meninges → Q07.9
  • Anomaly, anomalous (congenital) (unspecified type)nerve → Q07.9
  • Anomaly, anomalous (congenital) (unspecified type)nervous system (central) → Q07.9
  • Deformitymeninges or membrane (congenital) → Q07.9
  • Deformitynervous system (congenital) → Q07.9
  • Dysplasiabrain → Q07.9
  • Encephalopathy (acute)congenital → Q07.9
  • Lesion(s) (nontraumatic)nervous system, congenital → Q07.9
  • Maldevelopmentbrain → Q07.9
  • Malformation (congenital)dura → Q07.9
  • Malformation (congenital)meninges or membrane (congenital) → Q07.9
  • Malformation (congenital)nervous system (central) → Q07.9
  • Malformation (congenital)sense organs NEC → Q07.9
  • Arnold-Chiari disease, obstruction or syndrome (type II)withspina bifida → Q07.01
  • Malformation (congenital)ChiariType II → Q07.01
  • SyndromeDandy-Walkerwith spina bifida → Q07.01
  • Arnold-Chiari disease, obstruction or syndrome (type II)withhydrocephalus → Q07.02
  • Adhesions, adhesive (postinfective)meninges (cerebral) (spinal)congenital → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)choroidplexus → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)meningeal bands or foldsconstriction of → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)nerveacoustic → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)nerveoptic → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)opticnerve → Q07.8
  • Anomaly, anomalous (congenital) (unspecified type)spine, spinal NECnerve root → Q07.8

11 more, longer entries are not listed; the search box finds them by word.

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy