DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

Q03 Congenital hydrocephalus

  • Header · not billable

Q03 is not billable. The category heads 4 billable codes in FY2027: the 4 codes directly below it.

Index → code

  • Dandy-Walker syndrome → Q03.1
  • SyndromeDandy-Walker → Q03.1
  • DeformityDandy-Walker → Q03.1

Where it sits

  1. Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
  2. Q00-Q07 Congenital malformations of the nervous system (Q00-Q07)
  3. Q03 Congenital hydrocephalus
Billable codes
4
Subdivisions
4
CC / MCC codes
0 / 0
HCC V28 codes
4
New FY2027
0
Index entries
29

Codes in Q03

  1. Q03.0
    Malformations of aqueduct of Sylvius
    Billable182Exempt
    Inclusion terms 3

    Inclusion terms

    • Anomaly of aqueduct of Sylvius
    • Obstruction of aqueduct of Sylvius, congenital
    • Stenosis of aqueduct of Sylvius
  2. Q03.1
    Atresia of foramina of Magendie and Luschka
    Billable182Exempt
    Inclusion terms 1

    Inclusion terms

    • Dandy-Walker syndrome
  3. Q03.8
    Other congenital hydrocephalus
    Billable182Exempt
  4. Q03.9
    Congenital hydrocephalus, unspecified
    Billable182Exempt

Sources of each column.

Instructions

At Q03

Includes

  • hydrocephalus in newborn

Excludes1

  • Arnold-Chiari syndrome, type II (Q07.0-) Q07.0
  • acquired hydrocephalus (G91.-) G91
  • hydrocephalus due to congenital toxoplasmosis (P37.1) P37.1
  • hydrocephalus with spina bifida (Q05.0-Q05.4) Q05.0 Q05.4

Notes that also apply

Chapter 17 instructions (Notes 1, Excludes2 1): printed on the chapter 17 page.

Index entries

  • Dandy-Walker syndrome → Q03.1
  • Anomaly, anomalous (congenital) (unspecified type)aqueduct of Sylvius → Q03.0
  • Atresia, atreticaqueduct of Sylvius → Q03.0
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)aqueduct Sylvius stricture → Q03.0
  • Septum, septate (congenital)aqueduct of Sylvius → Q03.0
  • Stenosis, stenotic (cicatricial)aqueduct of Sylvius (congenital) → Q03.0
  • Strictureaqueduct of Sylvius (congenital) → Q03.0
  • Cyst (colloid) (mucous) (simple) (retention)Dandy-Walker → Q03.1
  • DeformityDandy-Walker → Q03.1
  • SyndromeDandy-Walker → Q03.1
  • Obstruction, obstructed, obstructiveforamen of Monro (congenital) → Q03.8
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal) → Q03.9
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)newborn → Q03.9
  • Obstruction, obstructed, obstructiveaqueduct of Sylviuscongenital → Q03.0
  • Occlusion, occludedaqueduct of Sylviuscongenital → Q03.0
  • Atresia, atreticforamen ofLuschka → Q03.1
  • Atresia, atreticforamen ofMagendie → Q03.1
  • Block, blockedforamen Magendie (acquired)congenital → Q03.1
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)foramen Magendie block (acquired)congenital → Q03.1
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent)congenital (external) (internal)specified NEC → Q03.8
  • Absence (of) (organ or part) (complete or partial)skull bone (congenital)withhydrocephalus → Q03.9
  • Agenesisskull (bone)withhydrocephalus → Q03.9
  • Anomaly, anomalous (congenital) (unspecified type)skullwithhydrocephalus → Q03.9
  • Degeneration, degenerativebrain (cortical) (progressive)incongenital hydrocephalus → Q03.9
  • Distortion(s) (congenital)skull bone(s) NECwithhydrocephalus → Q03.9
  • Hypoplasia, hypoplasticskull (bone)withhydrocephalus → Q03.9
  • Anomaly, anomalous (congenital) (unspecified type)boneskullwithhydrocephalus → Q03.9
  • Deformityskull (acquired)congenitalwithhydrocephalus → Q03.9
  • Imperfectclosure (congenital)skullwithhydrocephalus → Q03.9

NCHS Alphabetic Index. Index first, then the Tabular List.

Hierarchy