DxCodebookFY2027 · Oct 1, 2026 – Sep 30, 2027

Category · FY2027

D58 Other hereditary hemolytic anemias

  • Header · not billable

D58 is not billable. The category heads 5 billable codes in FY2027: the 5 codes directly below it.

Index → code

  • Stomatocytosis → D58.8
  • Hemoglobinopathy (mixed) → D58.2
  • Heinz body anemia, congenital → D58.2

Where it sits

  1. Chapter 3 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
  2. D55-D59 Hemolytic anemias (D55-D59)
  3. D58 Other hereditary hemolytic anemias
Billable codes
5
Subdivisions
5
CC / MCC codes
2 / 0
HCC V28 codes
0
New FY2027
0
Index entries
68

Codes in D58

  1. D58.0
    Hereditary spherocytosis
    Billable
    Inclusion terms 3

    Inclusion terms

    • Acholuric (familial) jaundice
    • Congenital (spherocytic) hemolytic icterus
    • Minkowski-Chauffard syndrome
  2. D58.1
    Hereditary elliptocytosis
    Billable
    Inclusion terms 2

    Inclusion terms

    • Elliptocytosis (congenital)
    • Ovalocytosis (congenital) (hereditary)
  3. D58.2
    Other hemoglobinopathies
    Billable
    Inclusion terms 7, Excludes1 7

    Inclusion terms

    • Abnormal hemoglobin NOS
    • Congenital Heinz body anemia
    • Hb-C disease
    • Hb-D disease
    • Hb-E disease
    • Hemoglobinopathy NOS
    • Unstable hemoglobin hemolytic disease

    Excludes1

    • familial polycythemia (D75.0) D75.0
    • Hb-M disease (D74.0) D74.0
    • hemoglobin E-beta thalassemia (D56.5) D56.5
    • hereditary persistence of fetal hemoglobin [HPFH] (D56.4) D56.4
    • high-altitude polycythemia (D75.1) D75.1
    • methemoglobinemia (D74.-) D74
    • other hemoglobinopathies with thalassemia (D56.8) D56.8
  4. D58.8
    Other specified hereditary hemolytic anemias
    BillableCC
    Inclusion terms 1

    Inclusion terms

    • Stomatocytosis
  5. D58.9
    Hereditary hemolytic anemia, unspecified
    BillableCC

CC/MCC: as a secondary diagnosis, unless the principal diagnosis is on the code’s PDX exclusion list (MS-DRG v44 Appendix C; list on the code card).

Sources of each column.

Instructions

At D58

Excludes1

  • hemolytic anemia of the newborn (P55.-) P55

Notes that also apply

Chapter 3 instructions (Excludes2 9): printed on the chapter 3 page.

Index entries

  • Spherocytosis (congenital) (familial) (hereditary) → D58.0
  • Dresbach's syndrome (elliptocytosis) → D58.1
  • Elliptocytosis (congenital) (hereditary) → D58.1
  • Heinz body anemia, congenital → D58.2
  • Hemoglobinopathy (mixed) → D58.2
  • Stomatocytosis → D58.8
  • Spherocytosis (congenital) (familial) (hereditary)hemoglobin disease → D58.0
  • SyndromeMinkowski-Chauffard → D58.0
  • Elliptocytosis (congenital) (hereditary)Hb C (disease) → D58.1
  • Elliptocytosis (congenital) (hereditary)hemoglobin disease → D58.1
  • SyndromeDresbach's (elliptocytosis) → D58.1
  • Abnormal, abnormality, abnormalitieshemoglobin (disease) → D58.2
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)Heinz body, congenital → D58.2
  • HemoglobinConstant Spring → D58.2
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)stomatocytosis → D58.8
  • Decrease (d)fragility of erythrocytes → D58.8
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)childhood → D58.9
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)hemolytic → D58.9
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)congenitalspherocytic → D58.0
  • Disease, diseasedhemoglobin or Hbspherocytosis → D58.0
  • Jaundice (yellow)newbornspherocytosis (congenital) → D58.0
  • Disease, diseasedhemoglobin or Hbelliptocytosis → D58.1
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)congenitalHeinz body → D58.2
  • Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute)in (due to)hemoglobinopathy NEC → D58.2 [M36.3]
  • Arthropathyin (due to)hemoglobinopathy NEC → D58.2 [M36.3]
  • Disease, diseasedhemoglobin or Hbabnormal (mixed) NEC → D58.2
  • Disease, diseasedhemoglobin or HbC (Hb-C) → D58.2
  • Disease, diseasedhemoglobin or HbConstant Spring → D58.2
  • Disease, diseasedhemoglobin or HbD (Hb-D) → D58.2
  • Disease, diseasedhemoglobin or HbE (Hb-E) → D58.2
  • Disease, diseasedhemoglobin or Hbunstable, hemolytic → D58.2
  • Disease, diseasedhemolytic (newborn)unstable hemoglobin → D58.2
  • Trait(s)hemoglobinabnormal NEC → D58.2
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)hemolyticspecified (hereditary) type NEC → D58.8
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)hemolyticStransky-Regala type → D58.8
  • Syndromehyperviscosity ( of serum)sclerothymic → D58.8
  • Abnormal, abnormality, abnormalitieserythrocytescongenital, with perinatal jaundice → D58.9
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)chronichemolytic → D58.9
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)congenitalhereditary hemolytic NOS → D58.9
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)hemolyticchronic → D58.9

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